THE OMENNS SYNDROME - HISTOLOGICAL, IMMUNOHISTOCHEMICAL AND ULTRASTRUCTURAL EVIDENCE FOR A PARTIAL T-CELL DEFICIENCY EVOLVING IN AN ABNORMAL PROLIFERATION OF LYMPHOCYTES-T AND S-100+/T-6+ LANGERHANS-LIKE CELLS

被引:30
作者
RUCO, LP
STOPPACCIARO, A
PEZZELLA, F
MIROLO, M
UCCINI, S
BARSOTTI, P
CASSANO, AM
BONER, AL
BUSINCO, L
DIFAZIO, A
BARONI, CD
机构
[1] UNIV LA SAPIENZA,SCH MED,DEPT HUMAN BIOPATHOL,IMMUNOPATHOL SECT,CHAIR PATHOL ANAT 4,I-00161 ROME,ITALY
[2] UNIV LA SAPIENZA,SCH MED,DEPT HUMAN BIOPATHOL,ULTRASTRUCT PATHOL SECT,I-00161 ROME,ITALY
[3] UNIV LA SAPIENZA,SCH MED,DEPT PEDIAT,I-00161 ROME,ITALY
[4] BORGO ROMA HOSP,DEPT PEDIAT,I-37134 VERONA,ITALY
关键词
D O I
10.1007/BF00701330
中图分类号
R602 [外科病理学、解剖学]; R32 [人体形态学];
学科分类号
100101 ;
摘要
引用
收藏
页码:69 / 82
页数:14
相关论文
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WOOD GS, 1983, J IMMUNOL, V131, P212
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WYSS, M ;
VONFLIEDNER, V ;
JACOTDESCOMBES, E ;
JEANNET, M ;
DESPONT, JP ;
KAPANCI, Y ;
COX, JN .
CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1982, 23 (01) :34-49