IMPROVED NEUROLOGIC FUNCTION AFTER LONG-TERM CORRECTION OF VITAMIN-E-DEFICIENCY IN CHILDREN WITH CHRONIC CHOLESTASIS

被引:117
作者
SOKOL, RJ
GUGGENHEIM, M
IANNACCONE, ST
BARKHAUS, PE
MILLER, C
SILVERMAN, A
BALISTRERI, WF
HEUBI, JE
机构
[1] UNIV COLORADO, SCH MED, DEPT PEDIAT, DIV CHILD NEUROL, DENVER, CO 80262 USA
[2] UNIV COLORADO, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
[3] CHILDRENS HOSP RES FDN, DIV PEDIAT GASTROENTEROL & NUTR, CINCINNATI, OH 45229 USA
[4] CHILDRENS HOSP RES FDN, DIV NEUROL, CINCINNATI, OH 45229 USA
[5] UNIV CINCINNATI, MED CTR, DEPT NEUROL, CINCINNATI, OH 45267 USA
关键词
D O I
10.1056/NEJM198512193132505
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1580 / 1586
页数:7
相关论文
共 47 条
[22]   FAMILIAL INTRAHEPATIC CHOLESTASIS ASSOCIATED WITH PROGRESSIVE NEUROMUSCULAR DISEASE AND VITAMIN-E-DEFICIENCY [J].
NAKAGAWA, M ;
TAZAWA, Y ;
KOBAYASHI, Y ;
YAMADA, M ;
SUZUKI, H ;
KONNO, T ;
TADA, K .
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 1984, 3 (03) :385-389
[23]  
NELSON JS, 1983, CIBA F SYMP, V101, P92
[24]   ULTRASTRUCTURAL AND HISTOCHEMICAL ABNORMALITIES OF SKELETAL-MUSCLE IN PATIENTS WITH CHRONIC VITAMIN-E-DEFICIENCY [J].
NEVILLE, HE ;
RINGEL, SP ;
GUGGENHEIM, MA ;
WEHLING, CA ;
STARCEVICH, JM .
NEUROLOGY, 1983, 33 (04) :483-488
[25]  
PENTSCHEW ANGEL, 1962, ACTA NEUROPATHOL, V1, P313
[26]   ARTERIOHEPATIC DYSPLASIA - BENIGN SYNDROME OF INTRA-HEPATIC CHOLESTASIS WITH MULTIPLE ORGAN INVOLVEMENT [J].
RIELY, CA ;
COTLIER, E ;
JENSEN, PS ;
KLATSKIN, G .
ANNALS OF INTERNAL MEDICINE, 1979, 91 (04) :520-527
[27]  
RIIS RC, 1981, AM J VET RES, V42, P74
[28]  
ROBISON WG, 1980, INVEST OPHTH VIS SCI, V19, P1030
[29]   A PROGRESSIVE NEUROLOGIC SYNDROME IN CHILDREN WITH CHRONIC LIVER-DISEASE [J].
ROSENBLUM, JL ;
KEATING, JP ;
PRENSKY, AL ;
NELSON, JS .
NEW ENGLAND JOURNAL OF MEDICINE, 1981, 304 (09) :503-508
[30]   CHOLESTYRAMINE THERAPY IN PATIENTS WITH A PAUCITY OF INTRAHEPATIC BILE DUCTS [J].
SHARP, HL ;
CAREY, JB ;
WHITE, JG ;
KRIVIT, W .
JOURNAL OF PEDIATRICS, 1967, 71 (05) :723-+