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HEPATIC PEROXISOMES ARE DEFICIENT IN INFANTILE REFSUM DISEASE - A CYTOCHEMICAL STUDY OF 4 CASES
被引:86
作者
:
ROELS, F
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
ROELS, F
CORNELIS, A
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
CORNELIS, A
POLLTHE, BT
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
POLLTHE, BT
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
AUBOURG, P
OGIER, H
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
OGIER, H
SCOTTO, J
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
SCOTTO, J
SAUDUBRAY, JM
论文数:
0
引用数:
0
h-index:
0
机构:
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
SAUDUBRAY, JM
机构
:
[1]
HOP NECKER ENFANTS MALAD,INSERM,U12,GENET MED CLIN,F-75730 PARIS 15,FRANCE
[2]
HOP ST VINCENT PAUL,F-75674 PARIS 14,FRANCE
[3]
HOP BICETRE,INSERM,U56,F-94270 KREMLIN BICETRE,FRANCE
来源
:
AMERICAN JOURNAL OF MEDICAL GENETICS
|
1986年
/ 25卷
/ 02期
关键词
:
D O I
:
10.1002/ajmg.1320250210
中图分类号
:
Q3 [遗传学];
学科分类号
:
071007 ;
090102 ;
摘要
:
引用
收藏
页码:257 / 271
页数:15
相关论文
共 54 条
[51]
TSAI SC, 1969, J BIOL CHEM, V244, P2682
[52]
THIORIDAZINE - A SELECTIVE INHIBITOR OF PEROXISOMAL BETA-OXIDATION INVIVO
VANDENBRANDEN, C
论文数:
0
引用数:
0
h-index:
0
VANDENBRANDEN, C
ROELS, F
论文数:
0
引用数:
0
h-index:
0
ROELS, F
[J].
FEBS LETTERS,
1985,
187
(02)
: 331
-
333
[53]
PHYTOL AND PEROXISOME PROLIFERATION
VANDENBRANDEN, C
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
VANDENBRANDEN, C
VAMECQ, J
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
VAMECQ, J
WYBO, I
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
WYBO, I
ROELS, F
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
ROELS, F
[J].
PEDIATRIC RESEARCH,
1986,
20
(05)
: 411
-
415
[54]
PEROXISOMAL BETA-OXIDATION FROM ENDOGENOUS SUBSTRATES - DEMONSTRATION THROUGH H2O2 PRODUCTION IN THE UNANESTHETIZED MOUSE
VANDENBRANDEN, C
论文数:
0
引用数:
0
h-index:
0
VANDENBRANDEN, C
KERCKAERT, I
论文数:
0
引用数:
0
h-index:
0
KERCKAERT, I
ROELS, F
论文数:
0
引用数:
0
h-index:
0
ROELS, F
[J].
BIOCHEMICAL JOURNAL,
1984,
218
(03)
: 697
-
702
←
1
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共 54 条
[51]
TSAI SC, 1969, J BIOL CHEM, V244, P2682
[52]
THIORIDAZINE - A SELECTIVE INHIBITOR OF PEROXISOMAL BETA-OXIDATION INVIVO
VANDENBRANDEN, C
论文数:
0
引用数:
0
h-index:
0
VANDENBRANDEN, C
ROELS, F
论文数:
0
引用数:
0
h-index:
0
ROELS, F
[J].
FEBS LETTERS,
1985,
187
(02)
: 331
-
333
[53]
PHYTOL AND PEROXISOME PROLIFERATION
VANDENBRANDEN, C
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
VANDENBRANDEN, C
VAMECQ, J
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
VAMECQ, J
WYBO, I
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
WYBO, I
ROELS, F
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LOUVAIN,CHIM PHYSIOL LAB,B-1200 BRUSSELS,BELGIUM
ROELS, F
[J].
PEDIATRIC RESEARCH,
1986,
20
(05)
: 411
-
415
[54]
PEROXISOMAL BETA-OXIDATION FROM ENDOGENOUS SUBSTRATES - DEMONSTRATION THROUGH H2O2 PRODUCTION IN THE UNANESTHETIZED MOUSE
VANDENBRANDEN, C
论文数:
0
引用数:
0
h-index:
0
VANDENBRANDEN, C
KERCKAERT, I
论文数:
0
引用数:
0
h-index:
0
KERCKAERT, I
ROELS, F
论文数:
0
引用数:
0
h-index:
0
ROELS, F
[J].
BIOCHEMICAL JOURNAL,
1984,
218
(03)
: 697
-
702
←
1
2
3
4
5
6
→