CYTOCHROME-OXIDASE DEFICIENCY - IMMUNOLOGICAL STUDIES OF SKELETAL-MUSCLE MITOCHONDRIAL FRACTIONS

被引:9
作者
SHEPHERD, IM
BIRCHMACHIN, MA
JOHNSON, MA
SHERRATT, HSA
AYNSLEYGREEN, A
DROSTE, M
KADENBACH, B
STEPHENSON, JBP
KING, MD
DICK, DJ
TURNBULL, DM
机构
[1] UNIV NEWCASTLE UPON TYNE, DEPT NEUROL, NEWCASTLE UPON TYNE NE1 7RU, TYNE & WEAR, ENGLAND
[2] UNIV NEWCASTLE UPON TYNE, DEPT PHARMACOL SCI, NEWCASTLE UPON TYNE NE1 7RU, TYNE & WEAR, ENGLAND
[3] UNIV NEWCASTLE UPON TYNE, DEPT CHILD HLTH, NEWCASTLE UPON TYNE NE1 7RU, TYNE & WEAR, ENGLAND
[4] UNIV MARBURG, BIOCHEM FACHBEREICH CHEM, D-3550 MARBURG, FED REP GER
[5] ROYAL HOSP SICK CHILDREN, FRASER ALLANDER UNIT PAEDIAT NEUROL, GLASGOW G3 8SJ, SCOTLAND
关键词
D O I
10.1016/0022-510X(88)90251-1
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:265 / 274
页数:10
相关论文
共 39 条
  • [21] THE CLINICAL-FEATURES OF MITOCHONDRIAL MYOPATHY
    PETTY, RKH
    HARDING, AE
    MORGANHUGHES, JA
    [J]. BRAIN, 1986, 109 : 915 - 938
  • [22] PERIPHERAL NEUROPATHY IN MITOCHONDRIAL DISEASE
    PEZESHKPOUR, G
    KRARUP, C
    BUCHTHAL, F
    DIMAURO, S
    BRESOLIN, N
    MCBURNEY, J
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1987, 77 (2-3) : 285 - 304
  • [23] CLINICAL PRESENTATION OF MITOCHONDRIAL RESPIRATORY-CHAIN DEFECTS IN NADH-COENZYME-Q REDUCTASE AND CYTOCHROME-OXIDASE - CLUES TO PATHOGENESIS OF LEIGH DISEASE
    ROBINSON, BH
    DEMEIRLEIR, L
    GLERUM, M
    SHERWOOD, G
    BECKER, L
    [J]. JOURNAL OF PEDIATRICS, 1987, 110 (02) : 216 - 222
  • [24] BIOSYNTHESIS OF MITOCHONDRIAL PROTEINS
    SCHATZ, G
    MASON, TL
    [J]. ANNUAL REVIEW OF BIOCHEMISTRY, 1974, 43 : 51 - 87
  • [25] NONDROPLET ULTRASTRUCTURAL DEMONSTRATION OF CYTOCHROME OXIDASE ACTIVITY WITH A POLYMERIZING OSMIOPHILIC REAGENT DIAMINOBENZIDINE (DAB)
    SELIGMAN, AM
    KARNOVSKY, MJ
    WASSERKRUG, HL
    HANKER, JS
    [J]. JOURNAL OF CELL BIOLOGY, 1968, 38 (01) : 1 - +
  • [26] MITOCHONDRIAL ENCEPHALOMYOPATHY AND PARTIAL CYTOCHROME-C-OXIDASE DEFICIENCY
    SERVIDEI, S
    LAZARO, RP
    BONILLA, E
    BARRON, KD
    ZEVIANI, M
    DIMAURO, S
    [J]. NEUROLOGY, 1987, 37 (01) : 58 - 63
  • [27] SHERRATT HSA, 1986, ANN NY ACAD SCI, V488, P508
  • [28] SHERRATT HSA, 1988, METHOD BIOCHEM ANAL, V33, P243
  • [29] PURIFICATION OF ALL 13 POLYPEPTIDES OF BOVINE HEART CYTOCHROME-C-OXIDASE FROM ONE ALIQUOT OF ENZYME - CHARACTERIZATION OF BOVINE FETAL HEART CYTOCHROME-C-OXIDASE
    TAKAMIYA, S
    LINDORFER, MA
    CAPALDI, RA
    [J]. FEBS LETTERS, 1987, 218 (02) : 277 - 282
  • [30] TANAKA M, 1986, ANN NY ACAD SCI, V488, P503