THE RELATIONSHIP BETWEEN THE BRANCHED-CHAIN AMINO-ACIDS AND THEIR ALPHA-KETOACIDS IN MAPLE SYRUP URINE DISEASE

被引：28

作者：

SNYDERMAN, SE

GOLDSTEIN, F

SANSARICQ, C

NORTON, PM

机构：

来源：

PEDIATRIC RESEARCH | 1984年 / 18卷 / 09期

关键词：

D O I：

10.1203/00006450-198409000-00009

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：851 / 853

页数：3

共 25 条

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[9] BRANCHED-CHAIN ALPHA-KETO ACIDS ISOLATED AS OXIME DERIVATIVES - RELATIONSHIP TO CORRESPONDING HYDROXY-ACIDS AND AMINO-ACIDS IN MAPLE SYRUP URINE DISEASE [J].

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