共 37 条
[2]
BRADFORD MM, 1976, ANAL BIOCHEM, V72, P248, DOI 10.1016/0003-2697(76)90527-3
[3]
BRADY RO, 1978, GENETIC BASIS INHERI
[4]
BURNETTE WN, 1981, ANAL BIOCHEM, V112, P195, DOI 10.1016/0003-2697(81)90281-5
[6]
ISOLATION OF 2 FORMS OF AN ACTIVATOR PROTEIN FOR THE ENZYMIC SPHINGOMYELIN DEGRADATION FROM HUMAN GAUCHER SPLEEN
[J].
BIOLOGICAL CHEMISTRY HOPPE-SEYLER,
1985, 366 (03)
:245-256
[7]
NIEMANN-PICK DISEASE, TYPE-C - EVIDENCE FOR THE DEFICIENCY OF AN ACTIVATING FACTOR STIMULATING SPHINGOMYELIN AND GLUCOCEREBROSIDE DEGRADATION
[J].
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE,
1980, 361 (10)
:1489-1502
[9]
PURIFICATION AND CHARACTERIZATION OF AN ACTIVATOR PROTEIN FOR THE DEGRADATION OF GLYCOLIPID-GM2 AND GLYCOLIPID-GA2 BY HEXOSAMINIDASE-A
[J].
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE,
1979, 360 (12)
:1837-1849