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ASPARTYLGLYCOSAMINURIA - AN INBORN ERROR OF GLYCOPROTEIN CATABOLISM
被引:18
作者
:
MAURY, CPJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,MED CHEM,SF-00170 HELSINKI 17,FINLAND
MAURY, CPJ
机构
:
[1]
UNIV HELSINKI,MED CHEM,SF-00170 HELSINKI 17,FINLAND
[2]
RINNEKOTI INST MENTALLY RETARDED,DEPT RES,ESPOO,FINLAND
来源
:
JOURNAL OF INHERITED METABOLIC DISEASE
|
1982年
/ 5卷
/ 04期
关键词
:
D O I
:
10.1007/BF02179139
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
引用
收藏
页码:192 / 196
页数:5
相关论文
共 49 条
[41]
ENZYMATIC CLEAVAGE OF 2-ACETAMIDO-I-(BETA'-L-ASPARTAMIDO)-I,2-DIDEOXY-BETA-D-GLUCOSE BY HUMAN PLASMA AND SEMINAL FLUID . FAILURE TO DETECT HETEROZYGOUS STATE FOR ASPARTYLGLYCOSAMINURIA
POLLITT, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Research Council Unit for Metabolic Studies in Psychiatry, University Department of Psychiatry, Middlewood Hospital
POLLITT, RJ
JENNER, FA
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Research Council Unit for Metabolic Studies in Psychiatry, University Department of Psychiatry, Middlewood Hospital
JENNER, FA
[J].
CLINICA CHIMICA ACTA,
1969,
25
(03)
: 413
-
&
[42]
ROWLEY BO, 1972, CLIN CHEM, V18, P951
[43]
ISOLATION OF LIVER N-ASPARTYL-BETA-GLUCOSAMINIDASE IN ASPARTYLGLUCOSAMINURIA
SAVOLAINEN, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT CLIN CHEM,SF-00290 HELSINKI,FINLAND
UNIV HELSINKI,DEPT CLIN CHEM,SF-00290 HELSINKI,FINLAND
SAVOLAINEN, H
[J].
BIOCHEMICAL JOURNAL,
1976,
153
(03)
: 749
-
750
[44]
IMPROVED THIN-LAYER CHROMATOGRAPHIC METHOD FOR URINARY OLIGOSACCHARIDE SCREENING
SEWELL, AC
论文数:
0
引用数:
0
h-index:
0
SEWELL, AC
[J].
CLINICA CHIMICA ACTA,
1979,
92
(03)
: 411
-
414
[45]
STUDIES ON N-ASPARTYL-BETA-GLUCOSAMINIDASE IN ASPARTYLGLYCOSAMINURIA
SOMER, H
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
SOMER, H
PALO, J
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
PALO, J
SAVOLAINEN, H
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
SAVOLAINEN, H
KONTTINEN, A
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
KONTTINEN, A
[J].
CLINICA CHIMICA ACTA,
1975,
60
(02)
: 219
-
221
[46]
SUGAHARA K, 1976, J BIOCHEM-TOKYO, V80, P195, DOI 10.1093/oxfordjournals.jbchem.a131264
[47]
CHARACTERIZATION OF 2 GLYCOASPARAGINES ISOLATED FROM URINE OF PATIENTS WITH ASPARTYLGLYCOSYLAMINURIA (AGU)
SUGAHARA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
SUGAHARA, K
FUNAKOSHI, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
FUNAKOSHI, S
FUNAKOSHI, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
FUNAKOSHI, I
AULA, P
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
AULA, P
YAMASHINA, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
YAMASHINA, I
[J].
JOURNAL OF BIOCHEMISTRY,
1975,
78
(04)
: 673
-
678
[48]
ENZYMATIC DETERMINATION OF URINARY ASPARTYLGLYCOSYLAMINE - RAPID AND SENSITIVE METHOD TO DETECT ASPARTYLCLYCOSYLAMINURIA (AGU)
SUGAHARA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
SUGAHARA, K
NISHIMURA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
NISHIMURA, K
AULA, P
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
AULA, P
YAMASHINA, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
YAMASHINA, I
[J].
CLINICA CHIMICA ACTA,
1976,
72
(02)
: 265
-
267
[49]
PURIFICATION AND PROPERTIES OF A BETA-ASPARTYL N-ACETYLGLUCOSYLAMINE AMIDOHYDROLASE FROM HEN OVIDUCT
TARENTINO, AL
论文数:
0
引用数:
0
h-index:
0
机构:
Division of Laboratories and Research, New York State Department of Health, Albany
TARENTINO, AL
MALEY, F
论文数:
0
引用数:
0
h-index:
0
机构:
Division of Laboratories and Research, New York State Department of Health, Albany
MALEY, F
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1969,
130
(1-2)
: 295
-
+
←
1
2
3
4
5
→
共 49 条
[41]
ENZYMATIC CLEAVAGE OF 2-ACETAMIDO-I-(BETA'-L-ASPARTAMIDO)-I,2-DIDEOXY-BETA-D-GLUCOSE BY HUMAN PLASMA AND SEMINAL FLUID . FAILURE TO DETECT HETEROZYGOUS STATE FOR ASPARTYLGLYCOSAMINURIA
POLLITT, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Research Council Unit for Metabolic Studies in Psychiatry, University Department of Psychiatry, Middlewood Hospital
POLLITT, RJ
JENNER, FA
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Research Council Unit for Metabolic Studies in Psychiatry, University Department of Psychiatry, Middlewood Hospital
JENNER, FA
[J].
CLINICA CHIMICA ACTA,
1969,
25
(03)
: 413
-
&
[42]
ROWLEY BO, 1972, CLIN CHEM, V18, P951
[43]
ISOLATION OF LIVER N-ASPARTYL-BETA-GLUCOSAMINIDASE IN ASPARTYLGLUCOSAMINURIA
SAVOLAINEN, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT CLIN CHEM,SF-00290 HELSINKI,FINLAND
UNIV HELSINKI,DEPT CLIN CHEM,SF-00290 HELSINKI,FINLAND
SAVOLAINEN, H
[J].
BIOCHEMICAL JOURNAL,
1976,
153
(03)
: 749
-
750
[44]
IMPROVED THIN-LAYER CHROMATOGRAPHIC METHOD FOR URINARY OLIGOSACCHARIDE SCREENING
SEWELL, AC
论文数:
0
引用数:
0
h-index:
0
SEWELL, AC
[J].
CLINICA CHIMICA ACTA,
1979,
92
(03)
: 411
-
414
[45]
STUDIES ON N-ASPARTYL-BETA-GLUCOSAMINIDASE IN ASPARTYLGLYCOSAMINURIA
SOMER, H
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
SOMER, H
PALO, J
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
PALO, J
SAVOLAINEN, H
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
SAVOLAINEN, H
KONTTINEN, A
论文数:
0
引用数:
0
h-index:
0
机构:
RINNEKOTI INST MENTALLY RETARDED,RES DEPT,MAJALAMPI,FINLAND
KONTTINEN, A
[J].
CLINICA CHIMICA ACTA,
1975,
60
(02)
: 219
-
221
[46]
SUGAHARA K, 1976, J BIOCHEM-TOKYO, V80, P195, DOI 10.1093/oxfordjournals.jbchem.a131264
[47]
CHARACTERIZATION OF 2 GLYCOASPARAGINES ISOLATED FROM URINE OF PATIENTS WITH ASPARTYLGLYCOSYLAMINURIA (AGU)
SUGAHARA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
SUGAHARA, K
FUNAKOSHI, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
FUNAKOSHI, S
FUNAKOSHI, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
FUNAKOSHI, I
AULA, P
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
AULA, P
YAMASHINA, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,HELSINKI,FINLAND
YAMASHINA, I
[J].
JOURNAL OF BIOCHEMISTRY,
1975,
78
(04)
: 673
-
678
[48]
ENZYMATIC DETERMINATION OF URINARY ASPARTYLGLYCOSYLAMINE - RAPID AND SENSITIVE METHOD TO DETECT ASPARTYLCLYCOSYLAMINURIA (AGU)
SUGAHARA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
SUGAHARA, K
NISHIMURA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
NISHIMURA, K
AULA, P
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
AULA, P
YAMASHINA, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HELSINKI,DEPT PATHOL,SF-00290 HELSINKI,FINLAND
YAMASHINA, I
[J].
CLINICA CHIMICA ACTA,
1976,
72
(02)
: 265
-
267
[49]
PURIFICATION AND PROPERTIES OF A BETA-ASPARTYL N-ACETYLGLUCOSYLAMINE AMIDOHYDROLASE FROM HEN OVIDUCT
TARENTINO, AL
论文数:
0
引用数:
0
h-index:
0
机构:
Division of Laboratories and Research, New York State Department of Health, Albany
TARENTINO, AL
MALEY, F
论文数:
0
引用数:
0
h-index:
0
机构:
Division of Laboratories and Research, New York State Department of Health, Albany
MALEY, F
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1969,
130
(1-2)
: 295
-
+
←
1
2
3
4
5
→