ATAXIA-TELANGIECTASIA - AN INHERITED DISORDER OF IONIZING-RADIATION SENSITIVITY IN MAN - PROGRESS IN THE ELUCIDATION OF THE UNDERLYING BIOCHEMICAL DEFECT

被引:202
作者
MCKINNON, PJ [1 ]
机构
[1] FLINDERS UNIV S AUSTRALIA,MED CTR,SCH BIOL SCI,BEDFORD PK,SA 5042,AUSTRALIA
关键词
D O I
10.1007/BF00281059
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
引用
收藏
页码:197 / 208
页数:12
相关论文
共 165 条
[81]   REGULATION OF THE CELLULAR ACTIN LEVELS IN RESPONSE TO CHANGES IN THE CELL-DENSITY IN ATAXIA TELANGIECTASIA LYMPHOBLASTOID-CELLS [J].
MCKINNON, PJ ;
BURGOYNE, LA .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1984, 119 (02) :561-566
[82]  
MCKINNON PJ, 1985, EUR J CELL BIOL, V39, P161
[83]   MEASUREMENT OF DNA POLYMERASE-BETA IN SKIN FIBROBLAST CELL-LINES FROM PATIENTS WITH ATAXIA TELANGIECTASIA [J].
MITCHELL, JB ;
KARAWYA, E ;
KINSELLA, TJ ;
WILSON, SH .
MUTATION RESEARCH, 1985, 146 (03) :295-300
[84]   IONIZING-RADIATION AND DNA-CHAIN ELONGATION IN ATAXIA TELANGIECTASIA LYMPHOBLASTOID-CELLS [J].
MOHAMED, R ;
FORD, M ;
LAVIN, MF .
MUTATION RESEARCH, 1986, 165 (02) :117-122
[85]   ATAXIA-TELANGIECTASIA CELL-EXTRACTS CONFER RADIORESISTANT DNA-SYNTHESIS ON CONTROL-CELLS [J].
MOHAMED, R ;
LAVIN, MF .
EXPERIMENTAL CELL RESEARCH, 1986, 163 (02) :337-348
[86]   DNA-REPLICATION AND REPAIR IN ATAXIA TELANGIECTASIA CELLS EXPOSED TO BLEOMYCIN [J].
MORRIS, C ;
MOHAMED, R ;
LAVIN, MF .
MUTATION RESEARCH, 1983, 112 (02) :67-74
[87]   ALTERED PROTEIN-SYNTHESIS IN ATAXIA-TELANGIECTASIA FIBROBLASTS [J].
MURNANE, JP ;
PAINTER, RB .
BIOCHEMISTRY, 1983, 22 (05) :1217-1222
[88]   COMPLEMENTATION OF THE DEFECTS IN DNA-SYNTHESIS IN IRRADIATED AND UNIRRADIATED ATAXIA-TELANGIECTASIA CELLS [J].
MURNANE, JP ;
PAINTER, RB .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (06) :1960-1963
[89]  
NAGASAWA H, 1985, MUTAT RES, V148, P71, DOI 10.1016/0027-5107(85)90209-X
[90]   COMPARISON OF KINETICS OF X-RAY-INDUCED CELL KILLING IN NORMAL, ATAXIA TELANGIECTASIA AND HEREDITARY RETINOBLASTOMA FIBROBLASTS [J].
NAGASAWA, H ;
LITTLE, JB .
MUTATION RESEARCH, 1983, 109 (02) :297-308