MAGNETIC-RESONANCE-IMAGING OF THE BRAIN AND SPINAL-CORD IN CEREBROTENDINOUS XANTHOMATOSIS

被引：13

作者：

BENCZE, KS ^{[1
]}

VANDEPOLDER, DR ^{[1
]}

PROCKOP, LD ^{[1
]}

机构：

[1] UNIV S FLORIDA,COLL MED,DEPT NEUROL,TAMPA,FL 33612

来源：

JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY | 1990年 / 53卷 / 02期

关键词：

D O I：

10.1136/jnnp.53.2.166

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

This reports a 40 year old man with cerebrotendinous xanthomatosis who had bilateral cataracts, enlarged Achilles tendons, progressive dementia, gait disturbance and peripheral neuropathy. Electroencephalography, electromyography, and magnetic resonance imaging (MRI) of the brain and spine were performed. Magnetic resonance imaging revealed cerebral, cerebellar and cervical cord atrophy and white matter involvement in the cerebrum and cerebellum correlating well with the clinical findings. To date there has been one previous report of MRI of the brain in cerebrotendinous xanthomatosis and none of the spinal cord.

引用

页码：166 / 167

页数：2

共 9 条

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