ROLE OF THE 26-HYDROXYLASE IN THE BIOSYNTHESIS OF BILE-ACIDS IN THE NORMAL STATE AND IN CEREBROTENDINOUS XANTHOMATOSIS - AN INVIVO STUDY

被引:50
作者
BJORKHEM, I
FAUSA, O
HOPEN, G
OFTEBRO, H
PEDERSEN, JI
SKREDE, S
机构
[1] UNIV OSLO,RIKSHOSP,MED DEPT A,OSLO,NORWAY
[2] UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
[3] UNIV BERGEN,HAUKELAND HOSP,MED DEPT B,N-5016 BERGEN,NORWAY
[4] UNIV OSLO,SCH MED,INST NUTR RES,OSLO,NORWAY
关键词
D O I
10.1172/JCI110742
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:142 / 148
页数:7
相关论文
共 25 条
[1]   BIOSYNTHESIS OF BILE-ACIDS IN MAN - HYDROXYLATION OF C27-STEROID SIDE-CHAIN [J].
BJORKHEM, I ;
GUSTAFSSON, J ;
JOHANSSON, G ;
PERSSON, B .
JOURNAL OF CLINICAL INVESTIGATION, 1975, 55 (03) :478-486
[2]   ON CONVERSION OF CHOLESTEROL TO 5BETA-CHOLESTANE-3ALPHA 7ALPHA-DIOL IN GUINEA PIG LIVER HOMOGENATES [J].
BJORKHEM, I ;
DANIELSSON, H ;
EINARSSON, K .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1967, 2 (03) :294-+
[3]   STEREOCHEMISTRY OF ENZYMATIC CONVERSION OF A DELTA4-3-OXOSTEROID INTO A 3-OXO-5BETA-STEROID - BILE ACIDS AND STEROIDS 208 [J].
BJORKHEM, I .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1969, 7 (03) :413-&
[4]   OMEGA-HYDROXYLATION OF STEROID SIDE-CHAIN IN BIOSYNTHESIS OF BILE-ACIDS [J].
BJORKHEM, I ;
GUSTAFSSON, J .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1973, 36 (01) :201-212
[5]  
BJORKHEM I, 1981, J LIPID RES, V22, P191
[6]   ON MECHANISM OF ENZYMATIC CONVERSION OF CHOLEST-5ENE-3BETA,7ALPHA-DIOL INTO 7ALPHA-HYDROXYCHOLEST-4-EN-3-ONE [J].
BJORKHEM, I .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1969, 8 (03) :337-&
[7]  
Bjorkhem I, 1976, Prog Liver Dis, V5, P215
[8]  
BJORKHEM I, 1979, J BIOL CHEM, V255, P2925
[9]   BILE-ACID METABOLISM [J].
DANIELSSON, H ;
SJOVALL, J .
ANNUAL REVIEW OF BIOCHEMISTRY, 1975, 44 :233-253