ACCUMULATION OF 7-ALPHA-HYDROXY-4-CHOLESTEN-3-ONE AND CHOLESTA-4,6-DIEN-3-ONE IN PATIENTS WITH CEREBROTENDINOUS XANTHOMATOSIS - EFFECT OF TREATMENT WITH CHENODEOXYCHOLIC ACID

被引：42

作者：

BJORKHEM, I

SKREDE, S

BUCHMANN, MS

EAST, C

GRUNDY, S

机构：

[1] NATL HOSP NORWAY,INST CLIN BIOCHEM,OSLO 1,NORWAY

[2] UNIV TEXAS,DEPT INTERNAL MED,DALLAS,TX 75235

[3] UNIV TEXAS,CTR HUMAN NUTR,DALLAS,TX 75235

来源：

HEPATOLOGY | 1987年 / 7卷 / 02期

关键词：

D O I：

10.1002/hep.1840070210

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

引用

页码：266 / 271

页数：6

共 22 条

[1]

AHLBERG J, 1981, J LIPID RES, V22, P410

[2] LONG-TERM TREATMENT OF CEREBROTENDINOUS XANTHOMATOSIS WITH CHENODEOXYCHOLIC ACID [J].

BERGINER, VM ;

SALEN, G ;

SHEFER, S .

NEW ENGLAND JOURNAL OF MEDICINE, 1984, 311 (26) :1649-1652

[3]

BIEMANN K, 1982, MASS SPECTROMETRY OR, P204

[4] ROLE OF THE 26-HYDROXYLASE IN THE BIOSYNTHESIS OF BILE-ACIDS IN THE NORMAL STATE AND IN CEREBROTENDINOUS XANTHOMATOSIS - AN INVIVO STUDY [J].

BJORKHEM, I ;

FAUSA, O ;

HOPEN, G ;

OFTEBRO, H ;

PEDERSEN, JI ;

SKREDE, S .

JOURNAL OF CLINICAL INVESTIGATION, 1983, 71 (01) :142-148

[5]

BJORKHEM I, 1981, J LIPID RES, V22, P191

[6] ASSAY OF LIVER MICROSOMAL CHOLESTEROL 7 ALPHA-HYDROXYLASE USING DEUTERATED CARRIER AND GAS CHROMATOGRAPHY MASS SPECTROMETRY [J].

BJORKHEM, I ;

DANIELSS.H .

ANALYTICAL BIOCHEMISTRY, 1974, 59 (02) :508-516

[7] ON SYNTHESIS AND METABOLISM OF CHOLEST-4-EN-7 ALPHA-OL-3-ONE - BILE ACIDS AND STEROIDS 156 [J].

BJORKHEM, I ;

DANIELSSON, H ;

ISSIDORIDES, C ;

KALLNER, A .

ACTA CHEMICA SCANDINAVICA, 1965, 19 (09) :2151-+

[8]

FOLCH J, 1957, J BIOL CHEM, V226, P497

[9] STUDIES IN THE STEROL GROUP .53. THE PREPARATION OF 7-HYDROXY-3-KETO-DELTA4-STEROIDS [J].

GREENHALGH, CW ;

HENBEST, HB ;

JONES, ERH .

JOURNAL OF THE CHEMICAL SOCIETY, 1952, (JUN) :2375-2380

[10]

MAKITA M., 1963, ANALYT BIOCHEM, V5, P523, DOI 10.1016/0003-2697(63)90072-1

← 1 2 3 →