HEMATOPOIETIC-CELL TRANSPLANTATION IN MURINE GLOBOID-CELL LEUKODYSTROPHY (THE TWITCHER MOUSE) - EFFECTS ON LEVELS OF GALACTOSYLCERAMIDASE, PSYCHOSINE, AND GALACTOCEREBROSIDES

被引：81

作者：

ICHIOKA, T

KISHIMOTO, Y

BRENNAN, S

SANTOS, GW

YEAGER, AM

机构：

[1] JOHN F KENNEDY INST,707 N BROADWAY,BALTIMORE,MD 21205

[2] JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205

[3] JOHNS HOPKINS UNIV,SCH MED,DEPT PEDIAT,BALTIMORE,MD 21205

[4] JOHNS HOPKINS UNIV,SCH MED,CTR ONCOL,BALTIMORE,MD 21205

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1987年 / 84卷 / 12期

关键词：

D O I：

10.1073/pnas.84.12.4259

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：4259 / 4263

页数：5

共 28 条

[1]

BAYEVER E, 1985, LANCET, V2, P471

[2] HEREDITARY LEUCODYSTROPHY IN THE MOUSE - THE NEW MUTANT TWITCHER [J].

DUCHEN, LW ;

EICHER, EM ;

JACOBS, JM ;

SCARAVILLI, F ;

TEIXEIRA, F .

BRAIN, 1980, 103 (SEP) :695-710

[3] ASSIGNMENT OF GENES TO REGIONS OF MOUSE CHROMOSOMES [J].

EICHER, EM ;

WASHBURN, LL .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1978, 75 (02) :946-950

[4] AN ACCUMULATION OF GALACTOCEREBROSIDE IN KIDNEY FROM MOUSE GLOBOID-CELL LEUKODYSTROPHY (TWITCHER) [J].

IDA, H ;

UMEZAWA, F ;

KASAI, E ;

ETO, Y ;

MAEKAWA, K .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1982, 109 (03) :634-638

[5] GLYCOLIPIDS OF THE SPINAL-CORD, SCIATIC-NERVE, AND SYSTEMIC ORGANS OF THE TWITCHER MOUSE [J].

IGISU, H ;

SUZUKI, K .

JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1984, 43 (01) :22-36

[6]

IGISU H, 1984, J LIPID RES, V25, P1000

[7] LIPIDS OF DEVELOPING BRAIN OF TWITCHER MOUSE - AN AUTHENTIC MURINE MODEL OF HUMAN KRABBE DISEASE [J].

IGISU, H ;

SHIMOMURA, K ;

KISHIMOTO, Y ;

SUZUKI, K .

BRAIN, 1983, 106 (JUN) :405-417

[8] PROGRESSIVE ACCUMULATION OF TOXIC METABOLITE IN A GENETIC LEUKODYSTROPHY [J].

IGISU, H ;

SUZUKI, K .

SCIENCE, 1984, 224 (4650) :753-755

[9] ABNORMAL ACCUMULATION OF GALACTOSYLCERAMIDE IN THE KIDNEY OF TWITCHER MOUSE [J].

IGISU, H ;

TAKAHASHI, H ;

SUZUKI, K ;

SUZUKI, K .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 110 (03) :940-944

[10] THE PATHOGENESIS OF GLOBOID-CELL LEUCODYSTROPHY IN PERIPHERAL-NERVE OF THE MOUSE MUTANT TWITCHER [J].

JACOBS, JM ;

SCARAVILLI, F ;

DEARANDA, FT .

JOURNAL OF THE NEUROLOGICAL SCIENCES, 1982, 55 (03) :285-304

← 1 2 3 →