ABNORMAL ACCUMULATION OF GALACTOSYLCERAMIDE IN THE KIDNEY OF TWITCHER MOUSE

被引:32
作者
IGISU, H
TAKAHASHI, H
SUZUKI, K
SUZUKI, K
机构
[1] YESHIVA UNIV ALBERT EINSTEIN COLL MED,ROSE F KENNEDY CTR RES MENTAL RETARDAT & HUMAN DEV,BRONX,NY 10461
[2] YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT PATHOL,BRONX,NY 10461
[3] YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT NEUROSCI,BRONX,NY 10461
关键词
D O I
10.1016/0006-291X(83)91053-7
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:940 / 944
页数:5
相关论文
共 16 条
[1]  
ABRAMSON MB, 1965, J BIOL CHEM, V240, P2389
[2]   HEPATIC GALACTOSYLCERAMIDE IN GLOBOID-CELL LEUKODYSTROPHY (KRABBES DISEASE) [J].
DAWSON, G .
LIPIDS, 1973, 8 (03) :154-156
[3]   HEREDITARY LEUCODYSTROPHY IN THE MOUSE - THE NEW MUTANT TWITCHER [J].
DUCHEN, LW ;
EICHER, EM ;
JACOBS, JM ;
SCARAVILLI, F ;
TEIXEIRA, F .
BRAIN, 1980, 103 (SEP) :695-710
[4]   QUANTITATIVE DENSITOMETRIC THIN-LAYER CHROMATOGRAPHY OF LIPIDS USING COPPER ACETATE REAGENT [J].
FEWSTER, ME ;
BURNS, BJ ;
MEAD, JF .
JOURNAL OF CHROMATOGRAPHY, 1969, 43 (01) :120-+
[5]  
FOLCH J, 1957, J BIOL CHEM, V226, P497
[6]  
IGISU H, 1983, BRAIN
[7]   THE TWITCHER MOUSE - DETERMINATION OF GENETIC STATUS BY GALACTOSYLCERAMIDASE ASSAYS ON CLIPPED TAIL [J].
KOBAYASHI, T ;
NAGARA, H ;
SUZUKI, K ;
SUZUKI, K .
BIOCHEMICAL MEDICINE, 1982, 27 (01) :8-14
[8]   THE TWITCHER MOUSE - AN ENZYMATICALLY AUTHENTIC MODEL OF HUMAN GLOBOID-CELL LEUKODYSTROPHY (KRABBE DISEASE) [J].
KOBAYASHI, T ;
YAMANAKA, T ;
JACOBS, JM ;
TEIXEIRA, F ;
SUZUKI, K .
BRAIN RESEARCH, 1980, 202 (02) :479-483
[9]   GLYCOSYLCERAMIDE SYNTHESIS IN THE DEVELOPING SPINAL-CORD AND KIDNEY OF THE TWITCHER MOUSE, AN ENZYMATICALLY AUTHENTIC MODEL OF HUMAN KRABBE DISEASE [J].
KODAMA, S ;
IGISU, H ;
SIEGEL, DA ;
SUZUKI, K .
JOURNAL OF NEUROCHEMISTRY, 1982, 39 (05) :1314-1318
[10]  
NORTON WT, 1965, ANN NY ACAD SCI, V122, P77