A NOVEL PATHWAY FOR BIOSYNTHESIS OF CHOLESTANOL WITH 7-ALPHA-HYDROXYLATED C-27-STEROIDS AS INTERMEDIATES, AND ITS IMPORTANCE FOR THE ACCUMULATION OF CHOLESTANOL IN CEREBROTENDINOUS XANTHOMATOSIS

被引:63
作者
SKREDE, S
BJORKHEM, I
BUCHMANN, MS
HOPEN, G
FAUSA, O
机构
[1] UNIV OSLO,RIKSHOSP,DEPT MED A,OSLO,NORWAY
[2] HUDDINGE UNIV HOSP,KAROLINSKA INST,RES CTR,S-14186 HUDDINGE,SWEDEN
[3] UNIV BERGEN,HAUKELAND HOSP,DEPT HUMAN GENET,N-5016 BERGEN,NORWAY
[4] HUDDINGE UNIV HOSP,KAROLINSKA INST,DEPT CLIN CHEM,S-14186 HUDDINGE,SWEDEN
关键词
D O I
10.1172/JCI111719
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:448 / 455
页数:8
相关论文
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