SYSTEMIC LUPUS-ERYTHEMATOSUS IN A PATIENT WITH PARTIAL LIPODYSTROPHY

被引:27
作者
FONT, J [1 ]
HERRERO, C [1 ]
BOSCH, X [1 ]
CERVERA, R [1 ]
INGELMO, M [1 ]
MASCARO, JM [1 ]
机构
[1] HOSP CLIN BARCELONA, DEPT DERMATOL, BARCELONA 36, SPAIN
关键词
D O I
10.1016/0190-9622(90)70042-G
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Systemic lupus erythematosus developed in a 35-year-old woman who had partial lipodystrophy since she was 7 years old. To our knowledge, this association has been reported only once. She also had hypocomplementemia, mesangiocapillary glomerulonephritis type II, and a serum assay with positive results for C3 nephritic factor. The association of partial lipodystrophy with other autoimmune disorders suggests an immunologic pathogenesis for this disease. © 1990, American Academy of Dermatology, Inc.. All rights reserved.
引用
收藏
页码:337 / 340
页数:4
相关论文
共 24 条
[11]   ACTIVATION OF THE CLASSIC COMPLEMENT PATHWAY IN PATIENTS WITH THE C-3 NEPHRITIC FACTOR [J].
MCLEAN, RH ;
SIEGEL, NJ ;
KASHGARIAN, M .
NEPHRON, 1980, 25 (02) :57-64
[12]  
NG YC, 1986, CLIN EXP IMMUNOL, V65, P450
[13]   HEREDITARY DEFICIENCY OF 3RD COMPONENT OF COMPLEMENT IN A CHILD WITH FEVER, SKIN RASH, AND ARTHRALGIAS - RESPONSE TO TRANSFUSION OF WHOLE-BLOOD [J].
OSOFSKY, SG ;
THOMPSON, BH ;
LINT, TF ;
GEWURZ, H .
JOURNAL OF PEDIATRICS, 1977, 90 (02) :180-186
[14]  
PETERS DK, 1973, LANCET, V2, P535
[15]   LOCALIZED LIPOATROPHY (ATROPHIC CONNECTIVE-TISSUE DISEASE PANNICULITIS) [J].
PETERS, MS ;
WINKELMANN, RK .
ARCHIVES OF DERMATOLOGY, 1980, 116 (12) :1363-1368
[16]   STUDIES REGARDING A POSSIBLE FUNCTION FOR VIRUSES IN THE PATHOGENESIS OF SYSTEMIC LUPUS-ERYTHEMATOSUS [J].
PINCUS, T .
ARTHRITIS AND RHEUMATISM, 1982, 25 (07) :847-856
[17]   PARTIAL LIPODYSTROPHY - METABOLIC STUDIES IN 3 PATIENTS [J].
PISCATELLI, RL ;
VIEWEG, WVR ;
HAVEL, RJ .
ANNALS OF INTERNAL MEDICINE, 1970, 73 (06) :963-+
[18]   PROGRESSIVE LIPODYSTROPHY - A CLINICAL STUDY OF 50 PATIENTS [J].
RAINERPO.J ;
STICKLER, GB .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1963, 106 (04) :356-+
[19]   MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS WITH PARTIAL LIPODYSTROPHY - DISCORDANT OCCURRENCE IN IDENTICAL-TWINS [J].
REICHEL, W ;
KOBBERLING, J ;
FISCHBACH, H ;
SCHELER, F .
KLINISCHE WOCHENSCHRIFT, 1976, 54 (02) :75-81
[20]   CASE OF LIPODYSTROPHY [J].
ROONEY, PJ .
BMJ-BRITISH MEDICAL JOURNAL, 1970, 2 (5707) :464-+