TRAFFICKING OF LYSOSOMAL-ENZYMES IN NORMAL AND DISEASE STATES

[1] ALEXANDER D, 1984, AM J HUM GENET, V36, P1001

[2] SYNTHESIS AND MATURATION OF CROSS-REACTIVE GLYCOPROTEIN IN FIBROBLASTS DEFICIENT IN ARYLSULFATASE A ACTIVITY [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 112 (01) : 198 - 205

[3] BARRANGER JA, 1984, MOL BASIS LYSOSOMAL, P311

[4] THE MANNOSE-6-PHOSPHATE RECEPTOR FOR LYSOSOMAL-ENZYMES IS CONCENTRATED IN CIS GOLGI CISTERNAE [J]. CELL, 1984, 36 (02) : 295 - 307

[5] DETECTION OF EARLY CHANGES IN ANDROGEN-INDUCED MOUSE RENAL BETA-GLUCURONIDASE MESSENGER RIBONUCLEIC-ACID USING CLONED COMPLEMENTARY DEOXYRIBONUCLEIC-ACID [J]. BIOCHEMISTRY, 1983, 22 (26) : 6049 - 6053

[6] AB-VARIANT OF INFANTILE GM2 GANGLIOSIDOSIS - DEFICIENCY OF A FACTOR NECESSARY FOR STIMULATION OF HEXOSAMINIDASE A-CATALYZED DEGRADATION OF GANGLIOSIDE GM2 AND GLYCOLIPID GA2 [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1978, 75 (08) : 3979 - 3983

[7] MOLECULAR DEFECT IN COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY IN MAN [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15): : 4535 - 4539

[8] INHIBITION OF LYSOSOMAL ALPHA-MANNOSIDASE BY SWAINSONINE, AN INDOLIZIDINE ALKALOID ISOLATED FROM SWAINSONA-CANESCENS [J]. BIOCHEMICAL JOURNAL, 1980, 191 (02) : 649 - 651

[9] ERICKSON AH, 1981, J BIOL CHEM, V256, P1224

[10] TRANSLOCATION OF A LYSOSOMAL-ENZYME ACROSS THE MICROSOMAL MEMBRANE REQUIRES SIGNAL RECOGNITION PARTICLE [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 115 (01) : 275 - 280

[1] ALEXANDER D, 1984, AM J HUM GENET, V36, P1001

[2] SYNTHESIS AND MATURATION OF CROSS-REACTIVE GLYCOPROTEIN IN FIBROBLASTS DEFICIENT IN ARYLSULFATASE A ACTIVITY [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 112 (01) : 198 - 205

[3] BARRANGER JA, 1984, MOL BASIS LYSOSOMAL, P311

[4] THE MANNOSE-6-PHOSPHATE RECEPTOR FOR LYSOSOMAL-ENZYMES IS CONCENTRATED IN CIS GOLGI CISTERNAE [J]. CELL, 1984, 36 (02) : 295 - 307

[5] DETECTION OF EARLY CHANGES IN ANDROGEN-INDUCED MOUSE RENAL BETA-GLUCURONIDASE MESSENGER RIBONUCLEIC-ACID USING CLONED COMPLEMENTARY DEOXYRIBONUCLEIC-ACID [J]. BIOCHEMISTRY, 1983, 22 (26) : 6049 - 6053

[6] AB-VARIANT OF INFANTILE GM2 GANGLIOSIDOSIS - DEFICIENCY OF A FACTOR NECESSARY FOR STIMULATION OF HEXOSAMINIDASE A-CATALYZED DEGRADATION OF GANGLIOSIDE GM2 AND GLYCOLIPID GA2 [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1978, 75 (08) : 3979 - 3983

[7] MOLECULAR DEFECT IN COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY IN MAN [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15): : 4535 - 4539

[8] INHIBITION OF LYSOSOMAL ALPHA-MANNOSIDASE BY SWAINSONINE, AN INDOLIZIDINE ALKALOID ISOLATED FROM SWAINSONA-CANESCENS [J]. BIOCHEMICAL JOURNAL, 1980, 191 (02) : 649 - 651

[9] ERICKSON AH, 1981, J BIOL CHEM, V256, P1224

[10] TRANSLOCATION OF A LYSOSOMAL-ENZYME ACROSS THE MICROSOMAL MEMBRANE REQUIRES SIGNAL RECOGNITION PARTICLE [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 115 (01) : 275 - 280