THE ALPHA-1-ANTITRYPSIN GENE AND EMPHYSEMA

被引:56
作者
PERLMUTTER, DH
PIERCE, JA
机构
[1] WASHINGTON UNIV, SCH MED, DEPT MED, ST LOUIS, MO 63110 USA
[2] WASHINGTON UNIV, SCH MED, DEPT CELL BIOL, ST LOUIS, MO 63110 USA
[3] WASHINGTON UNIV, SCH MED, DEPT PHYSIOL, ST LOUIS, MO 63110 USA
来源
AMERICAN JOURNAL OF PHYSIOLOGY | 1989年 / 257卷 / 04期
关键词
D O I
10.1152/ajplung.1989.257.4.L147
中图分类号
Q4 [生理学];
学科分类号
071003 ;
摘要
引用
收藏
页码:L147 / L162
页数:16
相关论文
共 123 条
  • [51] ERIKSSON S, 1964, ACTA MED SCAND, V175, P197
  • [52] INDICATIONS FOR PEDIATRIC LIVER-TRANSPLANTATION
    ESQUIVEL, CO
    IWATSUKI, S
    GORDON, RD
    MARSH, WW
    KONERU, B
    MAKOWKA, L
    TZAKIS, AG
    TODO, S
    STARZL, TE
    [J]. JOURNAL OF PEDIATRICS, 1987, 111 (06) : 1039 - 1045
  • [53] EVANS E, 1987, J BIOL CHEM, V262, P10850
  • [54] ULTRASTRUCTURE OF HEPATOCYTES IN ALPHA-1-ANTITRYPSIN DEFICIENCY WITH GENOTYPE PI--
    FELDMANN, G
    MARTIN, JP
    SESBOUE, R
    ROPARTZ, C
    PERELMAN, R
    NATHANSON, M
    SERINGE, P
    BENHAMOU, JP
    [J]. GUT, 1975, 16 (10) : 796 - 799
  • [55] FELDMANN G, 1974, GASTROENTEROLOGY, V67, P1214
  • [56] FLORENT C, 1981, GASTROENTEROLOGY, V81, P777
  • [57] XENOPUS OOCYTES CAN SYNTHESIZE BUT DO NOT SECRETE THE Z VARIANT OF HUMAN ALPHA-1-ANTITRYPSIN
    FOREMAN, RC
    JUDAH, JD
    COLMAN, A
    [J]. FEBS LETTERS, 1984, 168 (01) : 84 - 88
  • [59] THE FOS COMPLEX AND FOS-RELATED ANTIGENS RECOGNIZE SEQUENCE ELEMENTS THAT CONTAIN AP-1 BINDING-SITES
    FRANZA, BR
    RAUSCHER, FJ
    JOSEPHS, SF
    CURRAN, T
    [J]. SCIENCE, 1988, 239 (4844) : 1150 - 1153
  • [60] INVIVO CATABOLISM OF ALPHA-1-PROTEINASE INHIBITOR-TRYPSIN, ANTITHROMBIN III THROMBIN AND ALPHA-2-MACROGLOBULIN-METHYLAMINE
    FUCHS, HE
    SHIFMAN, MA
    PIZZO, SV
    [J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1982, 716 (02) : 151 - 157