THE NEUROPATHOLOGY OF RETT-SYNDROME - OVERVIEW 1994

被引:79
作者
ARMSTRONG, DD
机构
关键词
RETT SYNDROME; NEUROPATHOLOGY;
D O I
10.1055/s-2007-979736
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The syndrome which Andreas Rett and Bengt Hagberg first brought to our attention has been observed for eighteen years. It appears to be unlike any other disease of childhood. The original descriptions of Rett syndrome, as being autistic, degenerative and progressive are now. based on longitudinal observations, being questioned. In this paper the morphologic changes in the nervous system in Rett syndrome are summarized. The evidence against a degenerative process are presented, and the alterations are considered, along with the clinical features in terms of a possible arrest of brain development.
引用
收藏
页码:100 / 104
页数:5
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