I-CELL DISEASE - EVIDENCE FOR A MANNOSE 6-PHOSPHATE INDEPENDENT PATHWAY FOR TRANSLOCATION OF LYSOSOMAL-ENZYMES IN LYMPHOBLASTOID-CELLS

被引：18

作者：

TSUJI, A

OMURA, K

SUZUKI, Y

机构：

来源：

CLINICA CHIMICA ACTA | 1988年 / 176卷 / 01期

关键词：

D O I：

10.1016/0009-8981(88)90181-7

中图分类号：

R446 [实验室诊断]; R-33 [实验医学、医学实验];

学科分类号：

1001 ;

摘要：

引用

收藏

页码：115 / 121

页数：7

相关论文

共 15 条

[1] DURAND P, 1982, GENETIC ERRORS GLYCO, P191
[2] BIOSYNTHESIS AND INTRACELLULAR-TRANSPORT OF ALPHA-GLUCOSIDASE AND CATHEPSIN-D IN NORMAL AND MUTANT HUMAN-FIBROBLASTS
ELFERINK, RPJO
VANDOORNVANWAKEREN, J
STRIJLAND, A
REUSER, AJJ
TAGER, JM
[J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 153 (01): : 55 - 63
[3] HASILIK A, 1980, J BIOL CHEM, V255, P4946
[4] HASILIK A, 1980, J BIOL CHEM, V255, P4937
[5] MEMBRANE-BOUND N-ACETYL-BETA-GLUCOSAMINIDASE - DIFFERENT BINDING-SPECIFICITY IN CONTROL AND I-CELL DISEASE LIVERS
KATO, G
SUZUKI, Y
[J]. FEBS LETTERS, 1985, 193 (02) : 222 - 226
[6] MUCOLIPIDOSIS-III BETA-N-ACETYL-D-HEXOSAMINIDASE-A - PURIFICATION AND PROPERTIES
KRESS, BC
HIRANI, S
FREEZE, HH
LITTLE, L
MILLER, AL
[J]. BIOCHEMICAL JOURNAL, 1982, 207 (03) : 421 - 428
[7] SIMPLIFIED METHOD FOR CYANOGEN-BROMIDE ACTIVATION OF AGAROSE FOR AFFINITY CHROMATOGRAPHY
MARCH, SC
PARIKH, I
CUATRECASAS, P
[J]. ANALYTICAL BIOCHEMISTRY, 1974, 60 (01) : 149 - 152
[8] IS THERE A MECHANISM FOR INTRODUCING ACID-HYDROLASES INTO LIVER LYSOSOMES THAT IS INDEPENDENT OF MANNOSE 6-PHOSPHATE RECOGNITION - EVIDENCE FROM I-CELL DISEASE
OWADA, M
NEUFELD, EF
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1982, 105 (03) : 814 - 820
[9] CHANGES IN CARBOHYDRATE METABOLISM OF MITOGENICALLY STIMULATED HUMAN PERIPHERAL LYMPHOCYTES .1. STIMULATION BY PHYTOHAEMAGGLUTININ
ROOS, D
LOOS, JA
[J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1970, 222 (03) : 565 - &
[10] SAKURABA H, 1982, CLIN CHIM ACTA, V125, P275