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ZELLWEGER SYNDROME - BIOCHEMICAL AND MORPHOLOGICAL-STUDIES ON 2 PATIENTS TREATED WITH CLOFIBRATE
被引:72
作者
:
LAZAROW, PB
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
LAZAROW, PB
BLACK, V
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
BLACK, V
SHIO, H
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
SHIO, H
FUJIKI, Y
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
FUJIKI, Y
HAJRA, AK
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
HAJRA, AK
DATTA, NS
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
DATTA, NS
BANGARU, BS
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
BANGARU, BS
DANCIS, J
论文数:
0
引用数:
0
h-index:
0
机构:
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
DANCIS, J
机构
:
[1]
NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016
[2]
NYU,DEPT CELL BIOL,NEW YORK,NY 10016
[3]
ROCKEFELLER UNIV,NEW YORK,NY 10021
[4]
UNIV MICHIGAN,NEUROSCI LAB,ANN ARBOR,MI 48109
来源
:
PEDIATRIC RESEARCH
|
1985年
/ 19卷
/ 12期
关键词
:
D O I
:
10.1203/00006450-198512000-00030
中图分类号
:
R72 [儿科学];
学科分类号
:
100202 ;
摘要
:
引用
收藏
页码:1356 / 1364
页数:9
相关论文
共 66 条
[1]
PARTIAL DISASSEMBLY OF PEROXISOMES
ALEXSON, SEH
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
ALEXSON, SEH
FUJIKI, Y
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
FUJIKI, Y
SHIO, H
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
SHIO, H
LAZAROW, PB
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
LAZAROW, PB
[J].
JOURNAL OF CELL BIOLOGY,
1985,
101
(01)
: 294
-
304
[2]
MICROPEROXISOMES IN CENTRAL NERVOUS-SYSTEM OF POSTNATAL RAT
ARNOLD, G
论文数:
0
引用数:
0
h-index:
0
ARNOLD, G
HOLTZMAN, E
论文数:
0
引用数:
0
h-index:
0
HOLTZMAN, E
[J].
BRAIN RESEARCH,
1978,
155
(01)
: 1
-
17
[3]
TISSUE FRACTIONATION STUDIES .17. INTRACELLULAR DISTRIBUTION OF MONOAMINE OXIDASE ASPARTATE AMINOTRANSFERASE ALANINE AMINOTRANSFERASE D-AMINO ACID OXIDASE + CATALASE IN RAT-LIVER TISSUE
BAUDHUIN, P
论文数:
0
引用数:
0
h-index:
0
BAUDHUIN, P
BEAUFAY, H
论文数:
0
引用数:
0
h-index:
0
BEAUFAY, H
SELLINGER, OZ
论文数:
0
引用数:
0
h-index:
0
SELLINGER, OZ
RAHMANLI, Y
论文数:
0
引用数:
0
h-index:
0
RAHMANLI, Y
DEDUVE, C
论文数:
0
引用数:
0
h-index:
0
DEDUVE, C
WATTIAUX, R
论文数:
0
引用数:
0
h-index:
0
WATTIAUX, R
JACQUES, P
论文数:
0
引用数:
0
h-index:
0
JACQUES, P
[J].
BIOCHEMICAL JOURNAL,
1964,
92
(01)
: 179
-
+
[4]
BENDAYAN M, 1982, LAB INVEST, V47, P364
[5]
TOPOGRAPHICAL DISTRIBUTION OF LIPID BIOSYNTHETIC-ENZYMES ON PEROXISOMES (MICROBODIES)
BISHOP, JE
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
BISHOP, JE
SALEM, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
SALEM, M
HAJRA, AK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
HAJRA, AK
[J].
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES,
1982,
386
(MAY)
: 411
-
413
[6]
URINARY-EXCRETION OF DICARBOXYLIC-ACIDS FROM PATIENTS WITH THE ZELLWEGER SYNDROME - IMPORTANCE OF PEROXISOMES IN BETA-OXIDATION OF DICARBOXYLIC-ACIDS
BJORKHEM, I
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
BJORKHEM, I
BLOMSTRAND, S
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
BLOMSTRAND, S
HAGA, P
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
HAGA, P
KASE, BF
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
KASE, BF
PALONEK, E
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
PALONEK, E
PEDERSEN, JI
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
PEDERSEN, JI
STRANDVIK, B
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
STRANDVIK, B
WIKSTROM, SA
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
WIKSTROM, SA
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1984,
795
(01)
: 15
-
19
[7]
BOWEN P, 1964, B JOHNS HOPKINS HOSP, V114, P402
[8]
FATTY-ACID OXIDATION BY HUMAN-LIVER PEROXISOMES
BRONFMAN, M
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Cell Biology, Universidad Católica de Chile, Santiago
BRONFMAN, M
INESTROSA, NC
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Cell Biology, Universidad Católica de Chile, Santiago
INESTROSA, NC
LEIGHTON, F
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Cell Biology, Universidad Católica de Chile, Santiago
LEIGHTON, F
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1979,
88
(03)
: 1030
-
1036
[9]
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P344
[10]
BURNETTE WN, 1981, ANAL BIOCHEM, V112, P195, DOI 10.1016/0003-2697(81)90281-5
←
1
2
3
4
5
6
7
→
共 66 条
[1]
PARTIAL DISASSEMBLY OF PEROXISOMES
ALEXSON, SEH
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
ALEXSON, SEH
FUJIKI, Y
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
FUJIKI, Y
SHIO, H
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
SHIO, H
LAZAROW, PB
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
LAZAROW, PB
[J].
JOURNAL OF CELL BIOLOGY,
1985,
101
(01)
: 294
-
304
[2]
MICROPEROXISOMES IN CENTRAL NERVOUS-SYSTEM OF POSTNATAL RAT
ARNOLD, G
论文数:
0
引用数:
0
h-index:
0
ARNOLD, G
HOLTZMAN, E
论文数:
0
引用数:
0
h-index:
0
HOLTZMAN, E
[J].
BRAIN RESEARCH,
1978,
155
(01)
: 1
-
17
[3]
TISSUE FRACTIONATION STUDIES .17. INTRACELLULAR DISTRIBUTION OF MONOAMINE OXIDASE ASPARTATE AMINOTRANSFERASE ALANINE AMINOTRANSFERASE D-AMINO ACID OXIDASE + CATALASE IN RAT-LIVER TISSUE
BAUDHUIN, P
论文数:
0
引用数:
0
h-index:
0
BAUDHUIN, P
BEAUFAY, H
论文数:
0
引用数:
0
h-index:
0
BEAUFAY, H
SELLINGER, OZ
论文数:
0
引用数:
0
h-index:
0
SELLINGER, OZ
RAHMANLI, Y
论文数:
0
引用数:
0
h-index:
0
RAHMANLI, Y
DEDUVE, C
论文数:
0
引用数:
0
h-index:
0
DEDUVE, C
WATTIAUX, R
论文数:
0
引用数:
0
h-index:
0
WATTIAUX, R
JACQUES, P
论文数:
0
引用数:
0
h-index:
0
JACQUES, P
[J].
BIOCHEMICAL JOURNAL,
1964,
92
(01)
: 179
-
+
[4]
BENDAYAN M, 1982, LAB INVEST, V47, P364
[5]
TOPOGRAPHICAL DISTRIBUTION OF LIPID BIOSYNTHETIC-ENZYMES ON PEROXISOMES (MICROBODIES)
BISHOP, JE
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
BISHOP, JE
SALEM, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
SALEM, M
HAJRA, AK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109
HAJRA, AK
[J].
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES,
1982,
386
(MAY)
: 411
-
413
[6]
URINARY-EXCRETION OF DICARBOXYLIC-ACIDS FROM PATIENTS WITH THE ZELLWEGER SYNDROME - IMPORTANCE OF PEROXISOMES IN BETA-OXIDATION OF DICARBOXYLIC-ACIDS
BJORKHEM, I
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
BJORKHEM, I
BLOMSTRAND, S
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
BLOMSTRAND, S
HAGA, P
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
HAGA, P
KASE, BF
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
KASE, BF
PALONEK, E
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
PALONEK, E
PEDERSEN, JI
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
PEDERSEN, JI
STRANDVIK, B
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
STRANDVIK, B
WIKSTROM, SA
论文数:
0
引用数:
0
h-index:
0
机构:
KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN
WIKSTROM, SA
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1984,
795
(01)
: 15
-
19
[7]
BOWEN P, 1964, B JOHNS HOPKINS HOSP, V114, P402
[8]
FATTY-ACID OXIDATION BY HUMAN-LIVER PEROXISOMES
BRONFMAN, M
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Cell Biology, Universidad Católica de Chile, Santiago
BRONFMAN, M
INESTROSA, NC
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Cell Biology, Universidad Católica de Chile, Santiago
INESTROSA, NC
LEIGHTON, F
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Cell Biology, Universidad Católica de Chile, Santiago
LEIGHTON, F
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1979,
88
(03)
: 1030
-
1036
[9]
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P344
[10]
BURNETTE WN, 1981, ANAL BIOCHEM, V112, P195, DOI 10.1016/0003-2697(81)90281-5
←
1
2
3
4
5
6
7
→