ZELLWEGER SYNDROME - BIOCHEMICAL AND MORPHOLOGICAL-STUDIES ON 2 PATIENTS TREATED WITH CLOFIBRATE

被引：72

作者：

LAZAROW, PB

BLACK, V

SHIO, H

FUJIKI, Y

HAJRA, AK

DATTA, NS

BANGARU, BS

DANCIS, J

机构：

[1] NYU,SCH MED,DEPT PEDIAT,550 1ST AVE,NEW YORK,NY 10016

[2] NYU,DEPT CELL BIOL,NEW YORK,NY 10016

[3] ROCKEFELLER UNIV,NEW YORK,NY 10021

[4] UNIV MICHIGAN,NEUROSCI LAB,ANN ARBOR,MI 48109

来源：

PEDIATRIC RESEARCH | 1985年 / 19卷 / 12期

关键词：

D O I：

10.1203/00006450-198512000-00030

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：1356 / 1364

页数：9

共 66 条

[41]

MIURA S, 1984, J BIOL CHEM, V259, P6397

[42] CYANIDE-INSENSITIVE AND CLOFIBRATE ENHANCED BETA-OXIDATION OF DODECANEDIOIC ACID IN RAT-LIVER - AN INDICATION OF PEROXISOMAL BETA-OXIDATION OF N-DICARBOXYLIC ACIDS [J].

MORTENSEN, PB ;

KOLVRAA, S ;

GREGERSEN, N ;

RASMUSSEN, K .

BIOCHIMICA ET BIOPHYSICA ACTA, 1982, 713 (02) :393-397

[43]

MORTENSEN RM, 1983, THESIS ROCKEFELLER U

[44] THE CEREBROHEPATORENAL (ZELLWEGER) SYNDROME - INCREASED LEVELS AND IMPAIRED DEGRADATION OF VERY-LONG-CHAIN FATTY-ACIDS AND THEIR USE IN PRENATAL-DIAGNOSIS [J].

MOSER, AE ;

SINGH, I ;

BROWN, FR ;

SOLISH, GI ;

KELLEY, RI ;

BENKE, PJ ;

MOSER, HW .

NEW ENGLAND JOURNAL OF MEDICINE, 1984, 310 (18) :1141-1146

[45] STUDIES ON MICROPEROXISOMES .2. A CYTOCHEMICAL METHOD FOR LIGHT AND ELECTRON-MICROSCOPY [J].

NOVIKOFF, AB ;

NOVIKOFF, PM ;

DAVIS, C ;

QUINTANA, N .

JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY, 1972, 20 (12) :1006-1023

[46] PEROXISOMES IN ABSORPTIVE CELLS OF MAMMALIAN SMALL-INTESTINE [J].

NOVIKOFF, PM ;

NOVIKOFF, AB .

JOURNAL OF CELL BIOLOGY, 1972, 53 (02) :532-+

[47] STUDIES ON MICROPEROXISOMES .3. OBSERVATIONS ON HUMAN AND RAT HEPATOCYTES [J].

NOVIKOFF, PM ;

NOVIKOFF, AB ;

QUINTANA, N ;

DAVIS, C .

JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY, 1973, 21 (06) :540-558

[48] PEROXISOMAL BETA-OXIDATION OF LONG FATTY-ACIDS - EFFECTS OF HIGH-FAT DIETS [J].

OSMUNDSEN, H .

ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1982, 386 (MAY) :13-29

[49] CEREBRO-HEPATO-RENAL SYNDROME [J].

PASSARGE, E ;

MCADAMS, AJ .

JOURNAL OF PEDIATRICS, 1967, 71 (05) :691-+

[50] CONVERSION OF 3-ALPHA,7-ALPHA,12-ALPHA-TRIHYDROXY-5-BETA-CHOLESTANOIC ACID INTO CHOLIC-ACID BY RAT-LIVER PEROXISOMES [J].

PEDERSEN, JI ;

GUSTAFSSON, J .

FEBS LETTERS, 1980, 121 (02) :345-348

← 1 2 3 4 5 6 7 →