CHARACTERIZATION OF A NEW MODEL OF GM2-GANGLIOSIDOSIS (SANDHOFFS DISEASE) IN KORAT CATS

被引：56

作者：

NEUWELT, EA

JOHNSON, WG

BLANK, NK

PAGEL, MA

MASLENMCCLURE, C

MCCLURE, MJ

WU, PM

机构：

[1] OREGON HLTH SCI UNIV,DEPT SURG,DIV NEUROSURG,PORTLAND,OR 97201

[2] OREGON HLTH SCI UNIV,DEPT NEUROL,PORTLAND,OR 97201

[3] OREGON HLTH SCI UNIV,DEPT PATHOL,PORTLAND,OR 97201

[4] OREGON HLTH SCI UNIV,DEPT MED GENET,PORTLAND,OR 97201

[5] OREGON HLTH SCI UNIV,PORTLAND,OR 97201

[6] COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1985年 / 76卷 / 02期

关键词：

D O I：

10.1172/JCI111997

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：482 / 490

页数：9

共 35 条

[11]

JOHNSON WG, 1981, NEUROLOGY, V31, P87

[12]

JOHNSON WG, 1973, ENZYME THERAPY GENET, P120

[13]

KABACK MM, 1977, TAYSACHS DISEASE SCR, P267

[14]

KABACK MM, 1977, TAYSACHS DISEASE SCR, P276

[15] SPECIFIC BINDING OF I-125-LABELED BETA-HEXOSAMINIDASE-A TO RAT-BRAIN SYNAPTOSOMES [J].

KUSIAK, JW ;

TONEY, JH ;

QUIRK, JM ;

BRADY, RO .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1979, 76 (02) :982-985

[16]

LEVITAN M, 1977, TXB HUMAN GENETICS, P482

[17] METHODOLOGY PRIMARY ENZYME IMMUNOASSAY (PEIA) - STUDIES OF MUTANT ENZYME IN METACHROMATIC LEUKODYSTROPHY (PRIMARY ENZYME IMMUNOASSAY OF ARYLSULFATASE-A) [J].

NEUWELT, E ;

KOHLER, PF ;

AUSTIN, J .

IMMUNOCHEMISTRY, 1973, 10 (11) :767-773

[18]

Neuwelt E A, 1981, Methods Enzymol, V73, P550

[19] IS THERE A THERAPEUTIC ROLE FOR BLOOD-BRAIN-BARRIER DISRUPTION [J].

NEUWELT, EA ;

FRENKEL, EP .

ANNALS OF INTERNAL MEDICINE, 1980, 93 (01) :137-139

[20]

NEUWELT EA, 1984, FED PROC, V43, P214

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