PERIPHERAL NEUROMUSCULAR MANIFESTATIONS IN SYSTEMIC-SCLEROSIS (SCLERODERMA)

被引:58
作者
HIETAHARJU, A
JAASKELAINEN, S
KALIMO, H
HIETARINTA, M
机构
[1] UNIV TURKU, CENT HOSP, DEPT NEUROPHYSIOL, SF-20520 TURKU 52, FINLAND
[2] UNIV TURKU, CENT HOSP, DEPT NEUROPATHOL, SF-20520 TURKU 52, FINLAND
[3] UNIV TURKU, CENT HOSP, DEPT INTERNAL MED, SF-20520 TURKU 52, FINLAND
关键词
SCLERODERMA; PERIPHERAL NERVE DISEASES; MUSCULAR DISEASES; ELECTRONEUROMYOGRAPHY;
D O I
10.1002/mus.880161110
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Systemic sclerosis (scleroderma) is thought to be the least likely of the collagen vascular disorders to cause nervous system damage. We evaluated the peripheral neuromuscular manifestations in 32 patients with scleroderma. A clinically defined peripheral nervous system (PNS) lesion was manifest in 5 of 32 patients (16%), including 2 patients with trigeminal neuropathy and single cases of polyneuropathy, brachial plexopathy, and lumbosacral radiculopathy. Neurophysiological studies suggested subclinical PNS involvement in 6 additional patients (3 with distal axonal polyneuropathy, 1 with probable myopathy and superimposed polyneuropathy, 1 with trigeminal neuropathy, and 1 with focal ulnar neuropathy). Even though subjective muscular complaints were numerous (16 patients, 50%), a defined primary muscular disease could be demonstrated only in 5 patients (16%). Our results indicate that peripheral neuropathy in scleroderma is not as uncommon as previously estimated. (C) 1993 John Wiley & Sons, Inc.
引用
收藏
页码:1204 / 1212
页数:9
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