Late, painful, subungual hyperkeratosis in incontinentia pigmenti

被引:11
作者
Abimelec, P [1 ]
Rybojad, M [1 ]
Cambiaghi, S [1 ]
Moraillon, I [1 ]
CavelierBalloy, B [1 ]
Marx, C [1 ]
Morel, P [1 ]
机构
[1] HOP ST LOUIS,SERV DERMATOL,F-75475 PARIS,FRANCE
关键词
D O I
10.1111/j.1525-1470.1995.tb00197.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
The postpubertal appearance of subungual, painful keratotic tumors is a rare feature of incontinentia pigmenti. A patient affected by incontinentia pigmenti developed subungual, painful, nontumoral, hyperkeratotic lesions of the hands at 10 years of age. The mildness of the subungual lesions may be explained by the early stage of the disorder, but it is difficult to correlate the severity of the fingertip pain with the absence of true tumoral swelling. To our knowledge this is the youngest patient reported so far and the only one with a prepubertal expression of this puzzling disorder.
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收藏
页码:340 / 342
页数:3
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