DIFFUSE PULMONARY ARTERIOVENOUS MALFORMATION IN A CHILD WITH POLYSPLENIA SYNDROME

被引:7
作者
KAPUR, S
ROME, J
CHANDRA, RS
机构
[1] CHILDRENS HOSP,NATL MED CTR,DEPT CARDIOL,WASHINGTON,DC 20010
[2] GEORGE WASHINGTON UNIV,SCH MED,DEPT PEDIAT,WASHINGTON,DC 20052
[3] GEORGE WASHINGTON UNIV,SCH MED,DEPT PATHOL,WASHINGTON,DC 20052
来源
PEDIATRIC PATHOLOGY & LABORATORY MEDICINE | 1995年 / 15卷 / 03期
关键词
DIFFUSE PULMONARY ARTERIOVENOUS MALFORMATION; POLYSPLENIA;
D O I
10.3109/15513819509026982
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Pulmonary arteriovenous malformation (PAVM) is usually seen as a well-circumscribed cystic mass. In this communication we describe a diffuse arteriovenous malformation in a 5-month-old infant. The lesion was seen only at the microscopic level and was associated with abdominal heterotaxy, atrial situs solitus, polysplenia, interrupted inferior vena cava, atrial septal defect, and atrioventricular canal. This uncommon association may be within the spectrum of polysplenia syndrome.
引用
收藏
页码:463 / 468
页数:6
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