CHRONIC GRANULOMATOUS-DISEASE PRESENTING IN CHILDHOOD WITH PSEUDOMONAS-CEPACIA SEPTICEMIA

被引:37
作者
LACY, DE [1 ]
SPENCER, DA [1 ]
GOLDSTEIN, A [1 ]
WELLER, PH [1 ]
DARBYSHIRE, P [1 ]
机构
[1] CHILDRENS HOSP,BIRMINGHAM B16 8ET,W MIDLANDS,ENGLAND
关键词
D O I
10.1016/0163-4453(93)92271-W
中图分类号
R51 [传染病];
学科分类号
100401 ;
摘要
Two children who presented with fever, enlarged liver and spleen and ascites were found to have Pseudomonas cepacia septicaemia which proved fatal despite appropriate antibiotics and maximum supportive care. Chronic granulomatous disease of childhood (CGD) was subsequently diagnosed in both children. The possibility of CGD needs to be considered in any child with unexplained P. cepacia infection. © 1993 The British Society for the Study of Infection.
引用
收藏
页码:301 / 304
页数:4
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