VITAMIN-D-DEPENDENT RICKETS TYPE-II - DEFECTIVE INDUCTION OF 25-HYDROXYVITAMIN D3-24-HYDROXYLASE BY 1,25-DIHYDROXYVITAMIN D3 IN CULTURED SKIN FIBROBLASTS

被引:73
作者
GAMBLIN, GT
LIBERMAN, UA
EIL, C
DOWNS, RW
DEGRANGE, DA
MARX, SJ
机构
[1] USN HOSP,DEPT INTERNAL MED,ENDOCRINOL BRANCH,BETHESDA,MD 20814
[2] UNIFORMED SERV UNIV HLTH SCI,BETHESDA,MD 20814
[3] NIADDKD,METAB DIS BRANCH,BETHESDA,MD 20205
[4] BEILINSON MED CTR,TEL AVIV,ISRAEL
关键词
D O I
10.1172/JCI111796
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:954 / 960
页数:7
相关论文
共 46 条
  • [41] STIMULATION OF 24,25-DIHYDROXYVITAMIN-D3 PRODUCTION BY 1,25-DIHYDROXYVITAMIN-D3
    TANAKA, Y
    DELUCA, HF
    [J]. SCIENCE, 1974, 183 (4130) : 1198 - 1200
  • [42] TIETZE HU, 1981, ACTA ENDOCRINOL S, V240, P35
  • [43] REGULATION OF THE METABOLISM OF 25-HYDROXYVITAMIN-D3 IN PRIMARY CULTURES OF CHICK KIDNEY-CELLS
    TRECHSEL, U
    BONJOUR, JP
    FLEISCH, H
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (01) : 206 - 217
  • [44] AN UNUSUAL FORM OF VITAMIN-D-DEPENDENT RICKETS IN A CHILD - ALOPECIA AND MARKED END-ORGAN HYPOSENSITIVITY TO BIOLOGICALLY-ACTIVE VITAMIN-D
    TSUCHIYA, Y
    MATSUO, N
    CHO, H
    KUMAGAI, M
    YASAKA, A
    SUDA, T
    ORIMO, H
    SHIRAKI, M
    [J]. JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1980, 51 (04) : 685 - 690
  • [45] INVITRO SYNTHESIS OF 1-ALPHA, 25-DIHYDROXYCHOLECALCIFEROL AND 24,25-DIHYDROXYCHOLECALCIFEROL BY ISOLATED CALVARIAL CELLS
    TURNER, RT
    PUZAS, JE
    FORTE, MD
    LESTER, GE
    GRAY, TK
    HOWARD, GA
    BAYLINK, DJ
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (10): : 5720 - 5724
  • [46] UNIQUE FORM OF OSTEOMALACIA ASSOCIATED WITH END ORGAN REFRACTORINESS TO 1,25-DIHYDROXYVITAMIN-D AND APPARENT DEFECTIVE SYNTHESIS OF 25-HYDROXYVITAMIN-D
    ZERWEKH, JE
    GLASS, K
    JOWSEY, J
    PAK, CYC
    [J]. JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1979, 49 (02) : 171 - 175