STUDIES ON CYSTIC-FIBROSIS USING ISOELECTRIC FOCUSING .2. DEMONSTRATION OF DEFICIENT PROTEOLYTIC CLEAVAGE OF ALPHA2-MACROGLOBULIN IN CYSTIC-FIBROSIS PLASMA

被引:57
作者
WILSON, GB
FUDENBERG, HH
机构
[1] MED UNIV S CAROLINA,DEPT CLIN IMMUNOL & MICROBIOL,CHARLESTON,SC 29401
[2] UNIV CALIF,DEPT MED,SECT IMMUNOL,SAN FRANCISCO,CA 94122
关键词
D O I
10.1203/00006450-197602000-00003
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:87 / 96
页数:10
相关论文
共 53 条
[31]   STUDIES ON MECHANISM OF INHIBITION OF SODIUM TRANSPORT IN CYSTIC FIBROSIS OF PANCREAS [J].
MANGOS, JA ;
MCSHERRY, NR .
PEDIATRIC RESEARCH, 1968, 2 (05) :378-&
[32]   THE MODE OF ACTION OF HAGEMAN FACTOR IN THE RELEASE OF PLASMA KININ [J].
MARGOLIS, J .
JOURNAL OF PHYSIOLOGY-LONDON, 1960, 151 (02) :238-252
[33]  
MCCOMBS ML, 1973, TEX REP BIOL MED, V31, P615
[34]   INHIBITORS OF KALLIKREIN IN HUMAN PLASMA [J].
MCCONNELL, DJ .
JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (07) :1611-+
[35]  
MOLENAAR JL, 1974, J IMMUNOL, V112, P1444
[36]  
MUNRO GF, 1975, CYSTIC FIBROSIS CLUB, P7
[37]  
OUCHTERLONY O, 1974, HDB EXPT IMMUNOLOGY, P191
[38]   DEFICIENCY OF KALLIKREIN ACTIVITY IN PLASMA OF PATIENTS WITH CYSTIC-FIBROSIS [J].
RAO, GJS ;
NADLER, HL ;
POSNER, LA .
SCIENCE, 1972, 177 (4049) :610-&
[39]   ARGININE ESTERASE IN CYSTIC-FIBROSIS OF PANCREAS [J].
RAO, GJS ;
NADLER, HL .
PEDIATRIC RESEARCH, 1974, 8 (06) :684-686
[40]  
Ratnoff O D, 1969, Adv Immunol, V10, P145, DOI 10.1016/S0065-2776(08)60417-4