VISUAL-SYSTEM ABNORMALITIES IN ADRENOMYELONEUROPATHY

被引：19

作者：

KAPLAN, PW

KRUSE, B

TUSA, RJ

SHANKROFF, J

RIGNANI, J

MOSER, HW

机构：

[1] JOHNS HOPKINS UNIV, SCH MED, JOHNS HOPKINS HOSP, BALTIMORE, MD USA

[2] KENNEDY KRIEGER INST, BALTIMORE, MD USA

[3] UNIV FLORIDA, DEPT OTOLARYNGOL & OPHTHALMOL, MIAMI, FL USA

来源：

ANNALS OF NEUROLOGY | 1995年 / 37卷 / 04期

关键词：

D O I：

10.1002/ana.410370419

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

We studied the visual system in 59 men with adrenomyeloneuropathy. Pattern-reversal visual evoked potentials, magnetic resonance imaging, and clinical examination revealed that visual pathways are affected in 63% of patients, involving the optic discs, optic nerves, lateral geniculate bodies, optic radiations, and parietooccipital cortex. This indicates both primary demyelination of the optic nerves and discs, and more diffuse involvement of postchiasmal structures.

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页码：550 / 552

页数：3

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