PEROXISOMES AND HUMAN METABOLIC DISEASES - THE CEREBROHEPATORENAL SYNDROME (CHRS), CEREBROTENDINOUS XANTHOMATOSIS, AND SCHILDERS DISEASE (ADRENOLEUKODYSTROPHY)

被引:36
作者
GOLDFISCHER, S [1 ]
机构
[1] YESHIVA UNIV ALBERT EINSTEIN COLL MED,LIVER RES CTR,BRONX,NY 10461
关键词
D O I
10.1111/j.1749-6632.1982.tb21470.x
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:526 / 529
页数:4
相关论文
共 17 条
  • [1] BOEHME DH, 1982, PATHOL RES PRACT
  • [2] GOLDFISCHER S, 1981, GASTROENTEROLOGY, V81, P196
  • [3] GOLDFISCHER S, 1973, SCIENCE, V182, P52
  • [4] DEFECTS OF BILE-ACID SYNTHESIS IN ZELLWEGER SYNDROME
    HANSON, RF
    SZCZEPANIKVANLEEUWEN, P
    WILLIAMS, GC
    GRABOWSKI, G
    SHARP, HL
    [J]. SCIENCE, 1979, 203 (4385) : 1107 - 1108
  • [5] FATTY-ACID ABNORMALITY IN ADRENOLEUKODYSTROPHY
    IGARASHI, M
    SCHAUMBURG, HH
    POWERS, J
    KISHIMOTO, Y
    KOLODNY, E
    SUZUKI, K
    [J]. JOURNAL OF NEUROCHEMISTRY, 1976, 26 (04) : 851 - &
  • [6] LAZAROW PB, 1978, J BIOL CHEM, V253, P1522
  • [7] FATTY ACYL-COA OXIDIZING SYSTEM IN RAT-LIVER PEROXISOMES - ENHANCEMENT BY CLOFIBRATE, A HYPOLIPIDEMIC DRUG
    LAZAROW, PB
    DEDUVE, C
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (06) : 2043 - 2046
  • [8] 3 HYPOLIPIDEMIC DRUGS INCREASE HEPATIC PALMITOYL-COENZYME A OXIDATION IN RAT
    LAZAROW, PB
    [J]. SCIENCE, 1977, 197 (4303) : 580 - 581
  • [9] MASUI T, 1966, J BIOL CHEM, V241, P3889
  • [10] MATHIS RK, 1980, GASTROENTEROLOGY, V79, P1311