ADRENOLEUKODYSTROPHY - VERY LONG-CHAIN FATTY-ACID METABOLISM IN FIBROBLASTS

被引：57

作者：

RIZZO, WB

AVIGAN, J

CHEMKE, J

SCHULMAN, JD

机构：

[1] NICHHD,BIOCHEM GENET SECT,BETHESDA,MD 20205

[2] NHLBI,CELLULAR METAB LAB,BETHESDA,MD 20205

来源：

NEUROLOGY | 1984年 / 34卷 / 02期

关键词：

D O I：

10.1212/WNL.34.2.163

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：163 / 169

页数：7

共 19 条

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[6] HIGH-CONCENTRATION OF HEXACOSANOATE IN CULTURED SKIN FIBROBLAST LIPIDS FROM ADRENOLEUKODYSTROPHY PATIENTS [J].

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[7] ADRENOLEUKODYSTROPHY - EVIDENCE THAT ABNORMAL VERY LONG-CHAIN FATTY-ACIDS OF BRAIN CHOLESTEROL ESTERS ARE OF EXOGENOUS ORIGIN [J].

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[10] ADRENOLEUKODYSTROPHY - INCREASED PLASMA CONTENT OF SATURATED VERY LONG-CHAIN FATTY-ACIDS [J].

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