EPIDERMOLYSIS-BULLOSA ACQUISITA - A CASE WITH UPPER AIRWAYS OBSTRUCTION REQUIRING TRACHEOSTOMY AND RESPONDING TO CYCLOSPORINE

被引:18
作者
CLEMENT, M
RATNESAR, P
THIRUMOORTHY, T
MCGRATH, J
BLACK, MM
机构
[1] FARNBOROUGH HOSP, DEPT EAR NOSE & THROAT SURG, ORPINGTON BR6 8ND, KENT, ENGLAND
[2] NATL SKIN CTR, SINGAPORE, SINGAPORE
[3] ST THOMAS HOSP, ST JOHNS DERMATOL CTR, LONDON SE1 7EH, ENGLAND
关键词
D O I
10.1111/j.1365-2230.1993.tb01028.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
The case is reported of a 56-year-old man with epidermolysis bullosa acquisita (EBA) who developed such severe involvement of the upper respiratory tract that a tracheostomy had to be performed. Control of his disease was ultimately obtained with cyclosporin and the use of this drug in EBA is reviewed.
引用
收藏
页码:548 / 551
页数:4
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