共 29 条
[11]
MEISTER A, 1951, J BIOL CHEM, V190, P269
[13]
SCHADEWALDT P, 1989, BIOL CHEM H-S, V370, P951
[14]
FUNCTIONAL DIFFERENCES IN THE CATABOLISM OF BRANCHED-CHAIN L-AMINO-ACIDS IN CULTURED NORMAL AND MAPLE SYRUP URINE DISEASE FIBROBLASTS
[J].
BIOCHEMICAL MEDICINE AND METABOLIC BIOLOGY,
1989, 41 (02)
:105-116
[18]
SCRIVER CR, 1965, PEDIATRICS, V36, P592
[20]
SNYDERMAN SE, 1964, PEDIATRICS, V34, P454