MUTATIONS AFFECTING TRANSPORT AND STABILITY OF LYSOSOMAL-ENZYMES

被引：4

作者：

VONFIGURA, K ^{[1
]}

HASILIK, A ^{[1
]}

POHLMANN, R ^{[1
]}

BRAULKE, T ^{[1
]}

LEMANSKY, P ^{[1
]}

STEIN, M ^{[1
]}

机构：

[1] PHYSIOL CHEM INST,MUNSTER,FED REP GER

来源：

ENZYME | 1987年 / 38卷 / 1-4期

关键词：

D O I：

10.1159/000469200

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：144 / 153

页数：10

共 57 条

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[2] SULFATED OLIGOSACCHARIDES IN HUMAN LYSOSOMAL-ENZYMES
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[3] MANNOSE-6-PHOSPHATE RECEPTORS FOR LYSOSOMAL-ENZYMES CYCLE BETWEEN THE GOLGI-COMPLEX AND ENDOSOMES
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[J]. JOURNAL OF CELL BIOLOGY, 1986, 103 (04) : 1235 - 1247
[4] CAMPBELL CH, 1983, J BIOL CHEM, V258, P3347
[5] BIOCHEMICAL VARIABILITY OF ARYLSUFATASE -A, ARYLSULFASE-B AND ARYLSULFASE-C IN CULTURED FIBROBLASTS FROM PATIENTS WITH MULTIPLE SULFATASE DEFICIENCY
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[J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1983, 6 (04) : 167 - 172
[6] MOLECULAR DEFECT IN COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY IN MAN
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[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15): : 4535 - 4539
[7] DAZZO A, 1984, J BIOL CHEM, V259, P1070
[8] TRANSLOCATION OF A LYSOSOMAL-ENZYME ACROSS THE MICROSOMAL MEMBRANE REQUIRES SIGNAL RECOGNITION PARTICLE
ERICKSON, AH
WALTER, P
BLOBEL, G
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 115 (01) : 275 - 280
[9] HEXOSAMINIDASE A DEFICIENT ADULTS - PRESENCE OF ALPHA-CHAIN PRECURSOR IN CULTURED SKIN FIBROBLASTS
FRISCH, A
BARAM, D
NAVON, R
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1984, 119 (01) : 101 - 107
[10] INTERNALIZATION OF BLOCKING ANTIBODIES AGAINST MANNOSE-6-PHOSPHATE SPECIFIC RECEPTORS
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VONFIGURA, K
[J]. EMBO JOURNAL, 1985, 4 (07) : 1725 - 1730

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