HISTIOCYTIC TUMOR OF MECKELS CAVE - AN INTRACRANIAL EQUIVALENT OF JUVENILE XANTHOGRANULOMA OF THE SKIN

被引:34
作者
PAULUS, W
KIRCHNER, T
OTT, MM
KUHL, J
WARMUTHMETZ, M
SORENSEN, N
MULLERHERMELINK, HK
ROGGENDORF, W
机构
[1] UNIV WURZBURG, DEPT PATHOL, W-8700 WURZBURG, GERMANY
[2] UNIV WURZBURG, DEPT NEUROPATHOL, W-8700 WURZBURG, GERMANY
[3] UNIV WURZBURG, DEPT PEDIAT, W-8700 WURZBURG, GERMANY
[4] UNIV WURZBURG, DEPT NEURORADIOL, W-8700 WURZBURG, GERMANY
[5] UNIV WURZBURG, DEPT PEDIAT NEUROSURG, W-8700 WURZBURG, GERMANY
关键词
D O I
10.1097/00000478-199201000-00012
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
We present the case of a 7-year-old boy who had a solitary mass within Meckel's cave that recurred 6 weeks after the initial resection. The histological, immunohistochemical, electron-microscopical, and molecular genetical features established the lesion's histiocytic-nature. Our findings showed that it was closely related to juvenile xanthogranuloma, a benign lesion that usually occurs in the skin but has not yet been histologically confirmed in the brain. The present tumor is different from other intracranial histiocytic and xanthogranulomatous lesions.
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页码:76 / 83
页数:8
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