CYSTINOSIS - A DEFECT OF LYSOSOMAL CYSTINE EFFLUX

被引：2

作者：

SCHNEIDER, JA

机构：

来源：

BIOESSAYS | 1985年 / 2卷 / 04期

关键词：

D O I：

10.1002/bies.950020406

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：162 / 164

页数：3

共 29 条

[1]

BERGER EA, 1972, J BIOL CHEM, V247, P7684

[2]

BICKEL H, 1952, ACTA PAEDIATR SC S90, V42, P9

[3] CHARACTERISTICS OF CYSTINE COUNTER-TRANSPORT IN NORMAL AND CYSTINOTIC LYSOSOME-RICH LEUKOCYTE GRANULAR FRACTIONS [J].

GAHL, WA ;

TIETZE, F ;

BASHAN, N ;

BERNARDINI, I ;

RAIFORD, D ;

SCHULMAN, JD .

BIOCHEMICAL JOURNAL, 1983, 216 (02) :393-400

[4]

GAHL WA, 1982, J BIOL CHEM, V257, P9570

[5] CYSTINE TRANSPORT IS DEFECTIVE IN ISOLATED LEUKOCYTE LYSOSOMES FROM PATIENTS WITH CYSTINOSIS [J].

GAHL, WA ;

BASHAN, N ;

TIETZE, F ;

BERNARDINI, I ;

SCHULMAN, JD .

SCIENCE, 1982, 217 (4566) :1263-1265

[6] RUPTURE OF RAT-LIVER LYSOSOMES MEDIATED BY L-AMINO-ACID ESTERS [J].

GOLDMAN, R ;

KAPLAN, A .

BIOCHIMICA ET BIOPHYSICA ACTA, 1973, 318 (02) :205-216

[7]

JONAS AJ, 1983, J BIOL CHEM, V258, P1727

[8]

JONAS AJ, 1982, J BIOL CHEM, V257, P13185

[9] CYSTINE ACCUMULATION AND LOSS IN NORMAL, HETEROZYGOUS, AND CYSTINOTIC FIBROBLASTS [J].

JONAS, AJ ;

GREENE, AA ;

SMITH, ML ;

SCHNEIDER, JA .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (14) :4442-4445

[10]

JONAS AJ, 1983, FUNCTIONS GLUTATHION, P365

← 1 2 3 →