THE DESIGN OF A DIET RESTRICTED IN SATURATED VERY LONG-CHAIN FATTY-ACIDS - THERAPEUTIC APPLICATION IN ADRENOLEUKODYSTROPHY

被引:42
作者
VANDUYN, MA
MOSER, AE
BROWN, FR
SACKTOR, N
LIU, A
MOSER, HW
机构
关键词
D O I
10.1093/ajcn/40.2.277
中图分类号
R15 [营养卫生、食品卫生]; TS201 [基础科学];
学科分类号
100403 ;
摘要
引用
收藏
页码:277 / 284
页数:8
相关论文
共 21 条
  • [1] BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P164
  • [2] BIOSYNTHESIS OF VERY LONG-CHAIN FATTY-ACIDS BY SCIATIC-NERVE OF RABBIT
    CASSAGNE, C
    DARRIET, D
    BOURRE, JM
    [J]. FEBS LETTERS, 1978, 90 (02) : 336 - 340
  • [3] HILDITOH TP, 1964, CHEM CONSTITUTION NA
  • [4] FATTY-ACID ABNORMALITY IN ADRENOLEUKODYSTROPHY
    IGARASHI, M
    SCHAUMBURG, HH
    POWERS, J
    KISHIMOTO, Y
    KOLODNY, E
    SUZUKI, K
    [J]. JOURNAL OF NEUROCHEMISTRY, 1976, 26 (04) : 851 - &
  • [5] KAYSER S G, 1970, Biochemical and Biophysical Research Communications, V41, P1572, DOI 10.1016/0006-291X(70)90567-X
  • [6] ADRENOLEUKODYSTROPHY - EVIDENCE THAT ABNORMAL VERY LONG-CHAIN FATTY-ACIDS OF BRAIN CHOLESTEROL ESTERS ARE OF EXOGENOUS ORIGIN
    KISHIMOTO, Y
    MOSER, HW
    KAWAMURA, N
    PLATT, M
    PALLANTE, SL
    FENSELAU, C
    [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1980, 96 (01) : 69 - 76
  • [7] STRUCTURE AND BIOSYNTHESIS OF CUTICULAR LIPIDS - HYDROXYLATION OF PALMITIC ACID AND DECARBOXYLATION OF C28, C30, AND C32 ACIDS IN VICIA-FABA FLOWERS
    KOLATTUKUDY, PE
    CROTEAU, R
    BROWN, L
    [J]. PLANT PHYSIOLOGY, 1974, 54 (05) : 670 - 677
  • [8] ADRENOLEUKODYSTROPHY - ACCUMULATION OF CHOLESTEROL ESTERS WITH VERY LONG-CHAIN FATTY-ACIDS
    MENKES, JH
    CORBO, LM
    [J]. NEUROLOGY, 1977, 27 (10) : 928 - 932
  • [9] ACCUMULATION OF VERY LONG-CHAIN FATTY-ACIDS IS COMMON TO 3 VARIANTS OF ADRENOLEUKODYSTROPHY (ALD) - CLASSICAL ALD, ATYPICAL ALD (FEMALE PATIENT) AND ADRENOMYELONEUROPATHY
    MOLZER, B
    BERNHEIMER, H
    BUDKA, H
    PILZ, P
    TOIFL, K
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1981, 51 (02) : 301 - 310
  • [10] DETECTION OF ADRENOLEUKODYSTROPHY BY INCREASED C-26-0 FATTY-ACID LEVELS IN LEUKOCYTES
    MOLZER, B
    BERNHEIMER, H
    HELLER, R
    TOIFL, K
    VETTERLEIN, M
    [J]. CLINICA CHIMICA ACTA, 1982, 125 (03) : 299 - 305