BIOCHEMICAL AND HISTOPATHOLOGICAL STUDIES ON PATIENTS WITH MUCOPOLYSACCHARIDOSES, 2 OF WHOM HAD BEEN TREATED BY FIBROBLAST TRANSPLANTATION

被引:19
作者
CROW, J
GIBBS, DA
COZENS, W
SPELLACY, E
WATTS, RWE
机构
[1] MRC, CLIN RES CTR, DIV INHERITED METAB DIS, HARROW HA1 3UJ, MIDDX, ENGLAND
[2] NORTHWICK PK HOSP, DEPT HISTOPATHOL, HARROW HA1 3UJ, MIDDX, ENGLAND
关键词
D O I
10.1136/jcp.36.4.415
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
引用
收藏
页码:415 / 430
页数:16
相关论文
共 53 条
[21]   IDENTIFICATION OF ENZYMES THAT CATALYZE OXIDATION OF GLYOXYLATE TO OXALATE IN 100000 G SUPERNATANT FRACTION OF HUMAN HYPEROXALURIC AND CONTROL LIVER AND HEART TISSUE [J].
GIBBS, DA ;
WATTS, RWE .
CLINICAL SCIENCE, 1973, 44 (03) :227-+
[22]  
GIBBS DA, 1983, J INHER METAB DIS
[23]  
GIBBS DA, 1982, ADV TREATMENT INBORN
[24]   PATHOLOGIC FINDINGS IN MUCOPOLYSACCHARIDOSIS TYPE-IIIB (SANFILIPPOS SYNDROME-B) [J].
HADFIELD, MG ;
GHATAK, NR ;
NAKONECZNA, I ;
LIPPMAN, HR ;
MYER, EC ;
CONSTANTOPOULOS, G ;
BRADLEY, RM .
ARCHIVES OF NEUROLOGY, 1980, 37 (10) :645-650
[25]   ALPHA-L-IDURONIDASE ACTIVITY IN CULTURED SKIN FIBROBLASTS AND AMNIOTIC-FLUID CELLS [J].
HALL, CW ;
NEUFELD, EF .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 158 (02) :817-821
[26]   STUDIES OF SKIN IN HURLERS SYNDROME - MUCOPOLYSACCHARIDOSIS [J].
HAMBRICK, GW ;
SCHEIE, HG .
ARCHIVES OF DERMATOLOGY, 1962, 85 (04) :455-&
[27]  
HOBBS JR, 1981, LANCET, V2, P709
[28]  
HUG G, 1979, PHARMACOL REV, V30, P565
[29]   SEQUENTIAL THIN-LAYER CHROMATOGRAPHY OF URINARY ACIDIC GLYCOSAMINOGLYCANS [J].
HUMBEL, R ;
CHAMOLES, NA .
CLINICA CHIMICA ACTA, 1972, 40 (01) :290-&
[30]   THE NOMENCLATURE OF MUCOPOLYSACCHARIDES [J].
JEANLOZ, RW .
ARTHRITIS AND RHEUMATISM, 1960, 3 (03) :233-237