PROTEIN AND LEUCINE METABOLISM IN MAPLE SYRUP URINE DISEASE

被引:25
作者
THOMPSON, GN
BRESSON, JL
PACY, PJ
BONNEFONT, JP
WALTER, JH
LEONARD, JV
SAUDUBRAY, JM
HALLIDAY, D
机构
[1] CLIN RES CTR, NUTR RES GRP, HARROW HA1 3UJ, MIDDX, ENGLAND
[2] INST CHILD HLTH, DEPT CHILD HLTH, LONDON WC1N 2EH, ENGLAND
[3] HOP NECKER ENFANTS MALAD, GENET MED CLIN, F-75743 PARIS 15, FRANCE
来源
AMERICAN JOURNAL OF PHYSIOLOGY | 1990年 / 258卷 / 04期
关键词
D O I
10.1152/ajpendo.1990.258.4.E654
中图分类号
Q4 [生理学];
学科分类号
071003 ;
摘要
引用
收藏
页码:E654 / E660
页数:7
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