CAPILLARY GAS-CHROMATOGRAPHIC MASS-SPECTROMETRIC ANALYSIS OF ABNORMAL METABOLITES IN HYPOGLYCIN-TREATED RAT URINE

被引:11
作者
HINE, DG
TANAKA, K
机构
来源
BIOMEDICAL MASS SPECTROMETRY | 1984年 / 11卷 / 07期
关键词
D O I
10.1002/bms.1200110704
中图分类号
R318 [生物医学工程];
学科分类号
0831 ;
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页码:332 / 339
页数:8
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共 22 条
[11]   DEMONSTRATION OF A SPECIFIC MITOCHONDRIAL ISOVALERYL-COA DEHYDROGENASE-DEFICIENCY IN FIBROBLASTS FROM PATIENTS WITH ISOVALERIC ACIDEMIA [J].
RHEAD, WJ ;
TANAKA, K .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (01) :580-583
[12]   IDENTIFICATION OF BETA-HYDROXYISOVALERIC ACID IN URINE OF A PATIENT WITH ISOVALERIC ACIDEMIA [J].
TANAKA, K ;
ORR, JC ;
ISSELBACHER, KJ .
BIOCHIMICA ET BIOPHYSICA ACTA, 1968, 152 (03) :638-+
[13]  
TANAKA K, 1980, CLIN CHEM, V26, P1847
[14]   ISOVALERIC ACIDEMIA - A NEW GENETIC DEFECT OF LEUCINE METABOLISM [J].
TANAKA, K ;
BUDD, MA ;
EFRON, ML ;
ISSELBACHER, KJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1966, 56 (01) :236-+
[15]   HYPOGLYCIN-A - SPECIFIC INHIBITOR OF ISOVALERYL COA DEHYDROGENASE [J].
TANAKA, K ;
MILLER, EM ;
ISSELBAC.KJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1971, 68 (01) :20-+
[16]   ISOVALERIC AND ALPHA-METHYLBUTYRIC ACIDEMIAS INDUCED BY HYPOGLYCIN-A - MECHANISM OF JAMAICAN VOMITING SICKNESS [J].
TANAKA, K ;
SHIH, V ;
ISSELBACHER, KJ .
SCIENCE, 1972, 175 (4017) :69-+
[17]   JAMAICAN VOMITING SICKNESS - BIOCHEMICAL INVESTIGATION OF 2 CASES [J].
TANAKA, K ;
KEAN, EA ;
JOHNSON, B .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 295 (09) :461-467
[18]  
TANAKA K, 1967, J BIOL CHEM, V242, P2966
[19]  
TANAKA K, 1972, J BIOL CHEM, V247, P7465
[20]  
TANAKA K, 1979, HDB CLIN NEUROLOGY, V37, P511