共 13 条
[1]
AUERBACH VH, 1973, INBORN ERRORS METABO, P337
[4]
KETOTIC HYPOGLYCEMIA ASSOCIATED WITH TRANSIENT BRANCHED-CHAIN AMINOACIDEMIA
[J].
ACTA PAEDIATRICA SCANDINAVICA,
1972, 61 (01)
:81-+
[5]
HELD KR, 1976, MONATSSCHR KINDERH, V124, P59
[6]
INVESTIGATION OF METABOLIC PATTERN IN MAPLE SYRUP URINE DISEASE BY MEANS OF GLASS CAPILLARY GAS-CHROMATOGRAPHY AND MASS-SPECTROMETRY
[J].
JOURNAL OF CHROMATOGRAPHY,
1977, 143 (01)
:31-38
[7]
BRANCHED-CHAIN ALPHA-KETO ACIDS ISOLATED AS OXIME DERIVATIVES - RELATIONSHIP TO CORRESPONDING HYDROXY-ACIDS AND AMINO-ACIDS IN MAPLE SYRUP URINE DISEASE
[J].
METABOLISM-CLINICAL AND EXPERIMENTAL,
1974, 23 (03)
:257-265
[9]
MILLER LL, 1962, AMINO ACID POOLS, P708
[10]
ODESSEY R, 1974, J BIOL CHEM, V249, P7623