CHARACTERIZATION OF NEUTRAL AND ACIDIC GLYCOSPHINGOLIPIDS IN BRAINS OF 2 PATIENTS WITH GM1 GANGLIOSIDOSIS TYPE-1 AND TYPE-2

被引:4
作者
ISHIKAWA, Y
MAKITA, A
MINAMI, R
机构
[1] HOKKAIDO UNIV,SCH MED,INST CANC,BIOCHEM LAB,SAPPORO,HOKKAIDO 060,JAPAN
[2] SAPPORO MED COLL,DEPT PEDIAT,SAPPORO,HOKKAIDO 060,JAPAN
关键词
D O I
10.1111/j.1471-4159.1985.tb08730.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1100 / 1106
页数:7
相关论文
共 38 条
[31]  
VANCE DE, 1967, J LIPID RES, V8, P621
[32]   DISTRIBUTION OF LIPIDS IN HUMAN NERVOUS-SYSTEM .5. GANGLIOSIDES AND ALLIED NEUTRAL GLYCOLIPIDS OF INFANT BRAIN [J].
VANIER, MT ;
HOLM, M ;
MANSSON, JE ;
SVENNERHOLM, L .
JOURNAL OF NEUROCHEMISTRY, 1973, 21 (06) :1375-1384
[33]  
WENGER DA, 1980, CLIN GENET, V17, P323
[34]  
WOLFE LS, 1974, J BIOL CHEM, V249, P1828
[35]   GM1-GANGLIOSIDOSIS WITHOUT CHONDRODYSTROPHY OR VISCEROMEGALY . B-GALACTOSIDASE DEFICIENCY WITH GANGLIOSIDOSIS AND EXCESSIVE EXCRETION OF A KERATAN SULFATE [J].
WOLFE, LS ;
CALLAHAN, J ;
FAWCETT, JS ;
ANDERMANN, F ;
SCRIVER, CR .
NEUROLOGY, 1970, 20 (01) :23-+
[36]  
YAMASHITA K, 1981, J BIOL CHEM, V256, P4789
[37]   BLOOD-GROUP-A AND THE RELATED GLYCOLIPIDS OF HUMAN-LUNG [J].
YODA, Y ;
MAKITA, A ;
GASA, S .
JOURNAL OF BIOCHEMISTRY, 1982, 91 (02) :627-632
[38]  
1977, LIPIDS, V12, P455