BIOCHEMICAL VARIABILITY OF ARYLSUFATASE -A, ARYLSULFASE-B AND ARYLSULFASE-C IN CULTURED FIBROBLASTS FROM PATIENTS WITH MULTIPLE SULFATASE DEFICIENCY

被引:25
作者
CHANG, PL [1 ]
ROSA, NE [1 ]
BALLANTYNE, SR [1 ]
DAVIDSON, RG [1 ]
机构
[1] MCMASTER UNIV,DEPT PEDIAT,HAMILTON L8N 3Z5,ONTARIO,CANADA
关键词
D O I
10.1007/BF02310875
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:167 / 172
页数:6
相关论文
共 33 条
[31]  
SHAPIRO LJ, 1978, LANCET, V1, P70
[32]   MUCOPOLYSACCHARIDOSIS TYPE-VI - (MAROTEAUX-LAMY SYNDROME) .1. SULFATASE-B DEFICIENCY IN TISSUES [J].
STUMPF, DA ;
AUSTIN, JH ;
CROCKER, AC ;
LAFRANCE, M .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1973, 126 (06) :747-755
[33]  
YUTAKA T, 1981, CLIN GENET, V20, P296