PRION PROTEIN AMYLOID AND NEURODEGENERATION

被引:20
作者
PRUSINER, SB
DEARMOND, SJ
机构
[1] UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA 94143 USA
[2] UNIV CALIF SAN FRANCISCO, DEPT PATHOL, SAN FRANCISCO, CA 94143 USA
来源
AMYLOID-JOURNAL OF PROTEIN FOLDING DISORDERS | 1995年 / 2卷 / 01期
基金
美国国家卫生研究院;
关键词
PRION PROTEIN; CELLULAR ISOFORM OF PRP; SCRAPIE ISOFORM OF PRP; CREUTZFELDT-JAKOB DISEASE; GERSTMANN STRAUSSLER-SCHENKER DISEASE; FATAL FAMILIAL INSOMNIA; AMYOTROPHIC LATERAL SCLEROSIS; BOVINE SPONGIFORM ENCEPHALOPATHY; GLYCOSYLPHOSPHATIDYL INOSITOL; FOURIER TRANSFORM INFRARED; CIRCULAR DICHROISM; MOUSE; SYRIAN HAMSTER; HUMAN; WILDTYPE; TRANSGENIC; SCRAPIE-ASSOCIATED FIBRILS; HUMAN GROWTH HORMONE; RESTRICTION FRAGMENT LENGTH POLYMORPHISM;
D O I
10.3109/13506129509031887
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
[No abstract available]
引用
收藏
页码:39 / 65
页数:27
相关论文
共 254 条
[11]   ANTIBODIES TO A SCRAPIE PRION PROTEIN [J].
BENDHEIM, PE ;
BARRY, RA ;
DEARMOND, SJ ;
STITES, DP ;
PRUSINER, SB .
NATURE, 1984, 310 (5976) :418-421
[12]   IDENTIFICATION OF 2 BIOLOGICALLY DISTINCT STRAINS OF TRANSMISSIBLE MINK ENCEPHALOPATHY IN HAMSTERS [J].
BESSEN, RA ;
MARSH, RF .
JOURNAL OF GENERAL VIROLOGY, 1992, 73 :329-334
[13]   BIOCHEMICAL AND PHYSICAL-PROPERTIES OF THE PRION PROTEIN FROM 2 STRAINS OF THE TRANSMISSIBLE MINK ENCEPHALOPATHY AGENT [J].
BESSEN, RA ;
MARSH, RF .
JOURNAL OF VIROLOGY, 1992, 66 (04) :2096-2101
[14]   CREUTZFELDT-JAKOB DISEASE PRION PROTEINS IN HUMAN BRAINS [J].
BOCKMAN, JM ;
KINGSBURY, DT ;
MCKINLEY, MP ;
BENDHEIM, PE ;
PRUSINER, SB .
NEW ENGLAND JOURNAL OF MEDICINE, 1985, 312 (02) :73-78
[15]   IMMUNOBLOTTING OF CREUTZFELDT-JAKOB DISEASE PRION PROTEINS - HOST SPECIES-SPECIFIC EPITOPES [J].
BOCKMAN, JM ;
PRUSINER, SB ;
TATEISHI, J ;
KINGSBURY, DT .
ANNALS OF NEUROLOGY, 1987, 21 (06) :589-595
[16]   IDENTIFICATION OF A PROTEIN THAT PURIFIES WITH THE SCRAPIE PRION [J].
BOLTON, DC ;
MCKINLEY, MP ;
PRUSINER, SB .
SCIENCE, 1982, 218 (4579) :1309-1311
[17]   SCRAPIE AND CELLULAR PRION PROTEINS DIFFER IN THEIR KINETICS OF SYNTHESIS AND TOPOLOGY IN CULTURED-CELLS [J].
BORCHELT, DR ;
SCOTT, M ;
TARABOULOS, A ;
STAHL, N ;
PRUSINER, SB .
JOURNAL OF CELL BIOLOGY, 1990, 110 (03) :743-752
[18]  
BORCHELT DR, 1992, J BIOL CHEM, V267, P16188
[19]   RELEASE OF THE CELLULAR PRION PROTEIN FROM CULTURED-CELLS AFTER LOSS OF ITS GLYCOINOSITOL PHOSPHOLIPID ANCHOR [J].
BORCHELT, DR ;
ROGERS, M ;
STAHL, N ;
TELLING, G ;
PRUSINER, SB .
GLYCOBIOLOGY, 1993, 3 (04) :319-329
[20]  
Bouteille M, 1965, REV NEUROL, V118, P454