CEROID, LIPOFUSCIN AND THE CEROID-LIPOFUSCINOSES (BATTEN-DISEASE)

被引：23

作者：

JOLLY, RD

DALEFIELD, RR

PALMER, DN

机构：

[1] Department of Veterinary Pathology and Public Health, Massey University, Palmerston North

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1993年 / 16卷 / 02期

关键词：

D O I：

10.1007/BF00710265

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The similar histochemical, fluorescent and ultrastructural appearance of some lipofuscins and the pigment of Batten disease imply some underlying common chemical feature. The similar chloroform-methanol solubility of the protein subunit c in Batten disease and the specific proteins accumulated in thyroid lipofuscin imply that disordered or delayed catabolism of hydrophobic protein may be that common feature. © 1993 Society for the Study of Inborn Errors of Metabolism and Kluwer Academic Publishers.

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页码：280 / 283

页数：4

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