METABOLISM OF LOW-DENSITY LIPOPROTEINS BY CULTURED-HEPATOCYTES FROM NORMAL AND HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIC SUBJECTS

被引:21
作者
HOEG, JM
EDGE, SB
DEMOSKY, SJ
STARZL, TE
TRICHE, T
GREGG, RE
BREWER, HB
机构
[1] NCI,BETHESDA,MD 20892
[2] UNIV PITTSBURGH,SCH MED,DEPT SURG,PITTSBURGH,PA 15260
关键词
D O I
10.1016/0005-2760(86)90054-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:646 / 657
页数:12
相关论文
共 42 条
[11]   TYPE-III HYPERLIPOPROTEINEMIA ASSOCIATED WITH APOLIPOPROTEIN-E DEFICIENCY [J].
GHISELLI, G ;
SCHAEFER, EJ ;
GASCON, P ;
BREWER, HB .
SCIENCE, 1981, 214 (4526) :1239-1241
[12]   GENETIC-HETEROGENEITY IN FAMILIAL HYPERCHOLESTEROLEMIA - EVIDENCE FOR 2 DIFFERENT MUTATIONS AFFECTING FUNCTIONS OF LOW-DENSITY LIPOPROTEIN RECEPTOR [J].
GOLDSTEIN, JL ;
DANA, SE ;
BRUNSCHEDE, GY ;
BROWN, MS .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1975, 72 (03) :1092-1096
[13]  
GOLDSTEIN JL, 1983, NEW ENGL J MED, V309, P288, DOI 10.1056/NEJM198308043090507
[14]  
GOLDSTEIN JL, 1974, J BIOL CHEM, V249, P5153
[15]   DIFFERENCE IN SATURABLE BINDING OF LOW-DENSITY LIPOPROTEIN TO LIVER MEMBRANES FROM NORMOCHOLESTEROLEMIC SUBJECTS AND PATIENTS WITH HETEROZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA [J].
HARDERSPENGEL, K ;
WOOD, CB ;
THOMPSON, GR ;
MYANT, NB ;
SOUTAR, AK .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (20) :6355-6359
[16]   A SATURABLE, HIGH-AFFINITY BINDING-SITE FOR HUMAN LOW-DENSITY LIPOPROTEIN ON FRESHLY ISOLATED RAT HEPATOCYTES [J].
HARKES, L ;
VANBERKEL, TJC .
BIOCHIMICA ET BIOPHYSICA ACTA, 1982, 712 (03) :677-683
[17]   DISTRIBUTION AND CHEMICAL COMPOSITION OF ULTRACENTRIFUGALLY SEPARATED LIPOPROTEINS IN HUMAN SERUM [J].
HAVEL, RJ ;
EDER, HA ;
BRAGDON, JH .
JOURNAL OF CLINICAL INVESTIGATION, 1955, 34 (09) :1345-1353
[18]  
HEIDER JG, 1978, J LIPID RES, V19, P514
[19]   DISTINCT HEPATIC RECEPTORS FOR LOW-DENSITY LIPOPROTEIN AND APOLIPOPROTEIN-E IN HUMANS [J].
HOEG, JM ;
DEMOSKY, SJ ;
GREGG, RE ;
SCHAEFER, EJ ;
BREWER, HB .
SCIENCE, 1985, 227 (4688) :759-761
[20]   CHARACTERIZATION OF HEPATIC LOW-DENSITY LIPOPROTEIN BINDING AND CHOLESTEROL-METABOLISM IN NORMAL AND HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIC SUBJECTS [J].
HOEG, JM ;
DEMOSKY, SJ ;
SCHAEFER, EJ ;
STARZL, TE ;
BREWER, HB .
JOURNAL OF CLINICAL INVESTIGATION, 1984, 73 (02) :429-436