INVITRO RESPONSES TO ASCORBATE AND MANGANESE IN FIBROBLASTS FROM A PATIENT WITH PROLIDASE DEFICIENCY AND IMINODIPEPTIDURIA - CELL-GROWTH, PROLIDASE ACTIVITY AND COLLAGEN-METABOLISM

被引：30

作者：

MYARA, I

CHARPENTIER, C

WOLFROM, C

GAUTIER, M

LEMONNIER, A

LARREGUE, M

CHAMSON, A

FREY, J

机构：

[1] CHU BICETRE, INSERM, U56, UNITE RECH HEPATOL INFANTILE, F-94270 KREMLIN BICETRE, FRANCE

[2] UER MED, BIOCHIM LAB, F-42023 ST ETIENNE, FRANCE

[3] CHU POITIERS, F-86021 POITIERS, FRANCE

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1983年 / 6卷 / 01期

关键词：

D O I：

10.1007/BF02391189

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：27 / 31

页数：5

共 17 条

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[9] A SYNDROME RESEMBLING LATHYRISM ASSOCIATED WITH IMINODIPEPTIDURIA [J].

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