CEREBRAL PROTON MAGNETIC-RESONANCE SPECTROSCOPY IN RETT-SYNDROME

被引:25
作者
HANEFELD, F
CHRISTEN, HJ
HOLZBACH, U
KRUSE, B
FRAHM, J
HANICKE, W
机构
[1] MAX PLANCK INST BIOPHYS CHEM,BIOMED NMR FORSCH GMBH,W-3400 GOTTINGEN,GERMANY
[2] UNIV GOTTINGEN,KINDERKLIN,W-3400 GOTTINGEN,GERMANY
关键词
RETT SYNDROME; MR SPECTROSCOPY;
D O I
10.1055/s-2007-979742
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Combined MRI/MRS studies were performed in 9 girls with Rett syndrome of different ages. NAA, as marker of neuronal tissue, was found to decrease with increasing age. There was no evidence for a defective energy metabolism. The data point towards a probably secondary degenerative process in the pathogenesis of Rett syndrome.
引用
收藏
页码:126 / 127
页数:2
相关论文
共 12 条
[1]  
ARMSTRONG DD, 1992, BRAIN DEV S, V4, P89
[2]   RETT-SYNDROME - 3-D CONFOCAL MICROSCOPY OF CORTICAL PYRAMIDAL DENDRITES AND AFFERENTS [J].
BELICHENKO, PV ;
OLDFORS, A ;
HAGBERG, B ;
DAHLSTROM, A .
NEUROREPORT, 1994, 5 (12) :1509-1513
[3]   PROTON NMR-SPECTROSCOPY OF CEREBRAL METABOLIC ALTERATIONS IN INFANTILE PEROXISOMAL DISORDERS [J].
BRUHN, H ;
KRUSE, B ;
KORENKE, GC ;
HANEFELD, F ;
HANICKE, W ;
MERBOLDT, KD ;
FRAHM, J .
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1992, 16 (03) :335-344
[4]   IMPROVEMENTS IN LOCALIZED PROTON NMR-SPECTROSCOPY OF HUMAN BRAIN - WATER SUPPRESSION, SHORT ECHO TIMES, AND 1-ML RESOLUTION [J].
FRAHM, J ;
MICHAELIS, T ;
MERBOLDT, KD ;
BRUHN, H ;
GYNGELL, ML ;
HANICKE, W .
JOURNAL OF MAGNETIC RESONANCE, 1990, 90 (03) :464-473
[5]  
FRAHM J, 1991, MAGNETIC RESONANCE I, P165
[6]   ABSOLUTE CONCENTRATIONS OF METABOLITES IN THE ADULT HUMAN BRAIN INVIVO - QUANTIFICATION OF LOCALIZED PROTON MR SPECTRA [J].
MICHAELIS, T ;
MERBOLDT, KD ;
BRUHN, H ;
HANICKE, W ;
FRAHM, J .
RADIOLOGY, 1993, 187 (01) :219-227
[7]   CEREBELLAR AND CEREBRAL ABNORMALITIES IN RETT SYNDROME - A QUANTITATIVE MR ANALYSIS [J].
MURAKAMI, JW ;
COURCHESNE, E ;
HAAS, RH ;
PRESS, GA ;
YEUNGCOURCHESNE, R .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1992, 159 (01) :177-183
[8]   CEREBRAL MAGNETIC-RESONANCE SPECTROSCOPY IN RETT-SYNDROME - FAILURE TO DETECT MITOCHONDRIAL DISORDER [J].
NIELSEN, JB ;
TOFT, PB ;
RESKENIELSEN, E ;
JENSEN, KE ;
CHRISTIANSEN, P ;
THOMSEN, C ;
HENRIKSEN, O ;
LOU, HC .
BRAIN & DEVELOPMENT, 1993, 15 (02) :107-112
[9]   RETT SYNDROME - CEREBELLAR PATHOLOGY [J].
OLDFORS, A ;
SOURANDER, P ;
ARMSTRONG, DL ;
PERCY, AK ;
WITTENGERSTROM, I ;
HAGBERG, BA .
PEDIATRIC NEUROLOGY, 1990, 6 (05) :310-314
[10]  
PERCY AK, 1992, BRAIN DEV S, V14, P57