BILE-ACID ANALYSES IN PSEUDO-ZELLWEGER SYNDROME - CLUES TO THE DEFECT IN PEROXISOMAL BETA-OXIDATION

被引：39

作者：

CLAYTON, PT

LAKE, BD

HJELM, M

STEPHENSON, JBP

BESLEY, GTN

WANDERS, RJA

SCHRAM, AW

TAGER, JM

SCHUTGENS, RBH

LAWSON, AM

机构：

[1] ROYAL HOSP SICK CHILDREN,GLASGOW G3 8SJ,SCOTLAND

[2] ROYAL HOSP SICK CHILDREN,EDINBURGH EH9 1LF,MIDLOTHIAN,SCOTLAND

[3] UNIV AMSTERDAM,AMSTERDAM,NETHERLANDS

[4] CLIN RES CTR,HARROW HA1 3UJ,MIDDX,ENGLAND

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1988年 / 11卷

关键词：

D O I：

10.1007/BF01804226

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

收藏

页码：165 / 168

页数：4

相关论文

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