DEFICIENT PHOSPHORYLATION OF MANNOSE RESIDUES OF MANNAN IN FIBROBLASTS OF PATIENTS WITH MUCOLIPIDOSE-II AND MUCOLIPIDOSE-III

被引：5

作者：

BENYOSEPH, Y

HAHN, LC

DEFRANCO, CL

NADLER, HL

机构：

来源：

BIOCHEMICAL JOURNAL | 1981年 / 193卷 / 02期

关键词：

D O I：

10.1042/bj1930651

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：651 / 654

页数：4

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